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Spindle and Kinetochore-Associated Complex Is Associated With Poor Prognosis in Adrenocortical Carcinoma

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Shoukai Yu, PhD,* and Jun Ma, MD

Hongqiao International Institute of Medicine, Shanghai Tongren Hospital and Clinical Research Institute, Shanghai Jiao Tong University School of Medicine, Shanghai, China

ARTICLE INFO

Article history: Received 17 July 2021 Received in revised form 15 February 2022 Accepted 19 March 2022 Available online 21 April 2022

Keywords:

Adrenocortical carcinoma Cell cycle Prognosis Rare malignant tumor SKA complex

ABSTRACT

Introduction: The spindle and kinetochore-associated (SKA) complex, composed of three subunits (SKA1, SKA2, and SKA3), stabilizes spindle microtubule attachment to the kinetochore (KT) in the middle stage of mitosis. High expression of this complex is asso- ciated with poor prognosis for several tumors. However, the potential role of SKA complex overexpression in rare malignant diseases, such as adrenocortical carcinoma (ACC), has not been well investigated.

Materials and methods: In this study, we used several databases to explore the relationship between SKA subunit expression and prognosis in ACC patients. Gene ontology (GO) and Kyoto Encyclopedia of Genes and Genome (KEGG) databases were used to analyze enriched pathways in ACC.

Results: The results suggest that each of the three SKA subunits are overexpressed in ACC and that high expression is correlated with poor patient prognosis. Overexpression of the SKA complex is associated with the expression of organelle fission, nuclear division, and chromosome segregation pathways. Furthermore, differential expression of hub genes for proteins that interact physically or functionally with the SKA complex (CCNB2, UBE2C, BUB1B, TPX2, CCNA2, CDCA8, CCNB1, MELK, TOP2A, and KIF2C) revealed additional po- tential biomarkers for ACC.

Conclusions: Our findings provide additional understanding of the mechanisms of ACC and suggest an approach for biomarker discovery using publicly available resources.

@ 2022 Elsevier Inc. All rights reserved.

Introduction

Adrenocortical carcinoma (ACC) is a rare malignant disease with poor prognosis.1-4 It is an aggressive cancer that occurs in both children and adults.5 When identified in the early stages, ACC may be eligible for surgical removal; however, metastasis often occurs before diagnosis.6 Thus, biomarkers are needed for the early diagnosis, prognostic prediction, and develop- ment of new treatment approaches for ACC.7,8

The spindle and kinetochore-associated (SKA) complex, which is composed of three subunits (SKA1, SKA2, and SKA3), stabilizes spindle microtubule attachment to the kinetochore (KT) in the middle stage of mitosis.9,10 Dysre- gulation of the SKA complex is closely associated with the prognosis of malignant tumors such as breast cancer, cer- vical cancer, liver cancer, and lung cancer. In hepatocellu- lar carcinoma (HCC), there is a significant association between SKA1 overexpression and poor prognosis,

* Corresponding author. School of Medicine, Shanghai Jiao Tong University, Shanghai 200092, China. Tel .: /fax: 021-63846590. E-mail address: shoukaiyu@sjtu.edu.cn (S. Yu).

0022-4804/$ - see front matter @ 2022 Elsevier Inc. All rights reserved.

including correlations with tumor size and staging.11 In addition, upregulated SKA2 expression is associated with poor prognosis in breast cancer; SKA2 can affect the pro- liferation, migration, and invasion of breast cancer cells.12 In cervical cancer, the overexpression of SKA3 is also associated with poor prognosis and can affect proliferation, migration, and invasion.13 Despite this evidence for the role of the SKA complex in cancer, the potential clinical value of SKA proteins as biomarkers for ACC has not been investigated.

With the rapid development of microarray and ribo- nucleic acid (RNA) sequencing technology, research based on RNA expression plays an important role in biomedical investigation. Therefore, in this study, we unified a wide range of publicly available databases to investigate the expression of the SKA complex, explored correlations with prognosis, and evaluated potential mechanisms of regu- lation in ACC patients. We used the TCGA, ONCOMINE, cBioPortal, UALCAN, GEPIA, and STRING databases to obtain a comprehensive understanding of the structure and function of the SKA complex in ACC. In addition, we performed Gene ontology (GO), Kyoto Encyclopedia of Genes and Genomes (KEGG), and Protein-Protein Interac- tion (PPI) analyses to provide a mechanistic insight into the function of the SKA complex in ACC and investigated the potential clinical value of hub genes as biomarkers. Additional understanding of the role of the SKA complex in ACC provides a mechanistic insight and may further provide the development of new treatments for rare ma- lignant tumors.

Methods

Analysis of SKA subunit expression in ACC

RNA levels of the SKA complex in a variety of cancers were analyzed using ONCOMINE (www.oncomine.org), a cancer microarray database and a web-based translational data- mining platform for genome-wide expression analyses. The threshold was P < 0.0001 and multiple change = 1.5, with the analysis type set as tumor versus normal groups and the data type set as messenger RNA (mRNA). Additional expression data for ACC were evaluated using UALCAN, a web-portal for in-depth analyses of gene expression data from The Cancer Genome Atlas (TCGA; http://ualcan.path. uab.edu) and Gene Expression Profiling Interactive Anal- ysis (GEPIA), an open and straightforward database for investigating publicly available cancer transcriptome data. The expression of SKA1, SKA2, and SKA3 in paired ACC and normal tissue samples from TCGA database and the Genotype-Tissue Expression (GTEx) project was evaluated using UALCAN and GEPIA.14,15 Samples from UCSC XENA (https://xenabrowser.net/datapages/) were analyzed through Toil.16 Data in the form of TPM (transcripts per million) were converted to log2 (TPM + 1) for the analyses. The differential expression of SKA mRNA was evaluated via box plots and t-tests. Heatmaps were generated with R statistical software, version 3.6.3, using the ‘ggplot2’ package.

Analysis of cBioPortal

cBioPortal (www.cbioportal.org) for Cancer Genomics is a publicly available, open-source platform to explore cancer genome data; it provides visualization, analysis, and available downloads of large-scale multi omics cancer data. In this study, the cBioPortal database was used to analyze mRNA expression z-scores (RNA Seq V2 RSEM) of SKA genes.

Evaluation of the prognostic value of SKA gene expression in ACC

The potential clinical value of SKA upregulation in ACC pa- tients was evaluated by the Receiver Operator Characteristic (ROC) curve analysis. The expression data have been firstly ranked and split into two groups (high and low) for SKA members separately. Kaplan-Meier curves were generated to estimate the correlation between SKA complex expression and the overall survival (OS) of ACC patients. The associations of SKA gene expression with clinical characteristics of ACC were evaluated by the Pearson correlation. Further examina- tion using the clinical data from TCGA led to the identification of diagnostic and prognostic biomarkers for ACC.

Analysis of SKA-associated genes and pathways dysregulated in ACC

The gene expression data of 79 ACC patients were down- loaded from TCGA. Pearson correlation coefficients (|r| > 0.4 and P < 0.001) were applied to measure and identify genes coexpressed with SKA genes. Venn diagrams were imple- mented using Webtools (http://bioinformatics.p-sb.ugent.be/ webtools/Venn/) to identify genes correlated with all three SKA subunits. Potential biological functions and signaling pathways related to SKA genes were explored using the “clusterProfiler” package in R software.17 GO and KEGG ana- lyses were conducted for differentially expressed genes. For the GO analysis, biological process (BP), cellular composition (CC), and molecular function (MF) were applied, with P < 0.05 considered statistically significant.

Identification of an SKA-associated protein-protein interaction) network

The STRING database (http://string-db.org) was used to assess and integrate a protein-protein interaction (PPI) network for SKA coexpressed genes. The network included direct (phys- ical) and indirect (functional) associations with scores more than 0.7 considered significant.18 Cytoscape 3.8 (http://www. cytoscape.org) and CytoHubba plug-ins were implemented to identify the top 10 upregulated and downregulated hub genes.19-21 The ROC curves were plotted to analyze the prog- nostic ability of hub proteins in combinations, as a combina- tion of genes might improve the area under curve (AUC) values. Additional statistical analyses (t-test and rank sum test) and visualization were conducted using the R package and GraphPad Prism 7,22,23 with P values less than 0.05 considered significant.

Analysis Type by CancerCancer V5. Normal SKA1Cancer V5. Normal SKA2Cancer V5. Normal SKA3
Bladder Cancer
Brain and CNS Cancer141
Breast Cancer61315
Cervical Cancer1
Colorectal Cancer8113
Esophageal Cancer
Gastric Cancer2
Head and Neck Cancer1
Kidney Cancer3
Leukemia11
Liver Cancer1
Lung Cancer511
Lymphoma3
Melanoma
Myeloma
Other Cancer23
Ovarian Cancer1
Pancreatic Cancer
Prostate Cancer1
Sarcoma1
Significant Unique Analyses27217322
Total Unique Analyses368271281

1

5

10

10

5

1

☒ ☒ ☒

☐ %

☐ ☒ ☒

Fig. 1 - The mRNA expression of the spindle and kinetochore-associated (SKA) complex in various tumors from the ONCOMINE database. Red represents upregulation of the target gene, whereas blue represents downregulation. Threshold parameter settings were set at P value = 0.0001 and multiple change = 1.5.

Fig. 2 - The mRNA expression of spindle and kinetochore-associated (SKA) complex subunits in adrenocortical carcinoma (ACC) and normal control samples from the UALCAN, GTEx, and TCGA databases. (A) SKA1, (B) SKA2, and (C) SKA3. *** , P < 0.001.

A

B

7

C




6

3.5

6

The expression of SKA1 Log2 (TPM+1)

5

The expression of SKA2

3.0

5

4

Log2 (TPM+1)

The expression of SKA3

Log2 (TPM+1)

2.5

4

2.0

3

3

1.5

2

2

1.0

1

1

0.5

0

0

0.0

Normal

ACC

Normal ACC

Normal ACC

Results

The SKA complex is overexpressed in ACC

To determine whether the SKA complex may serve as a biomarker for ACC, we compared the mRNA levels for each of the SKA subunits for a variety of tumors and normal tissues from control patients using the ONCOMINE database. The mRNA levels of SKA1, SKA2, and SKA3 were elevated in several tumors, including breast, lung, and colorectal cancer, whereas other tumor types (bladder cancer, esophageal can- cer, melanoma, myeloma, and pancreatic cancer) showed no evidence of dysregulation (Fig. 1). These results are consistent with the results of previous studies9,24 and suggest that upregulation of SKA complex components is a common characteristic for specific cancer types.

To determine whether the trend of SKA upregulation is recapitulated in some cancers,11,13,24 we combined results from the UALCAN, GTEx, and TCGA databases. The over- expression of SKA1, SKA2, and SKA3 mRNAs was statisti- cally higher in the ACC patients versus normal groups (Fig. 2) using Wilcoxon rank sum tests. Further analysis demon- strated that the genetic alteration rates were 1.3% for SKA1, 5% for SKA2, and 8% for SKA3, with an increased expression for mRNA levels for all three SKA subunits in a subset of the ACC tumor samples (Fig. S1), compared to normal adrenal tissues.

To evaluate the predictive value of increased SKA expression in ACC, we performed the ROC analysis. The AUC was 0.818 for SKA1, 0.755 for SKA2, and 0.834 for SKA3, indicating poor overall survival for patients with elevated SKA complex expression (P < 0.05, Fig. 3). Furthermore, an analysis of the GEPIA database confirmed that ACC patients

Fig. 3 - The diagnostic value of the spindle and kinetochore-associated (SKA) complex in adrenocortical carcinoma (ACC) patients. The Receiver Operator Characteristic (ROC) analysis was performed to evaluate the predictive value of SKA subunit expression for the survival of ACC patients. (A) SKA1. (B) SKA2. (C) SKA3. AUC = area under curve; CI = confidence interval; FPR = false positive rate; TPR = true positive rate.

A

1.0

B

1.0

C

1.0

0.8

0.8

0.8

Sensitivity (TPR)

Sensitivity (TPR)

Sensitivity (TPR)

0.6

0.6

0.6

0.4

0.4

0.4

0.2

SKA1

0.2

SKA2

0.2

SKA3

AUC: 0.818

AUC: 0.755

AUC: 0.834

0.0

CI: 0.755-0.881

0.0

CI: 0.674-0.837

0.0

Cl: 0.771-0.897

0.0

0.2

0.4

0.6

0.8

1.0

0.0

0.2

0.4

0.6

0.8

1.0

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0.8

1.0

1-Specificity (FPR)

1-Specificity (FPR)

1-Specificity (FPR)

Fig. 4 - The correlation of spindle and kinetochore-associated (SKA) complex expression with overall survival of adrenocortical carcinoma (ACC) patients. Kaplan-Meier survival curves are shown for high and low expression groups for SKA1 (A), SKA2 (B), and SKA3 (C). The data were obtained from the GEPA database. HR = hazard ratio. The numbers at a risk for each group at each time point in the Kaplan-Meier curves were provided in Supplementary Table 2.

A

B

C

1.0

SKA1

1.0

SKA2

1.0

SKA3

Low

Low

Low

High

High

High

Survival probability

0.8

Survival probability

0.8

Survival probability

0.8

0.6

0.6

0.6

0.4

0.4

0.4

0.2

Overall Survival

0.2

Overall Survival

0.2

Overall Survival

HR = 6.20 (2.48-15.47)

HR = 3.85 (1.67-8.84)

HR = 6.14 (2.46-15.30)

0.0

P < 0.001

0.0

P = 0.002

0.0

P < 0.001

0

1000

2000

3000

4000

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2000

3000

4000

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1000

2000

3000

4000

Time (days)

Time (days)

Time (days)

with higher expression of the SKA complex subunits tended to have worse overall survival than those with low expres- sion (P < 0.01; Fig. 4 and Table S1). An analysis of the tumor characteristics of the patients suggested that SKA1 and SKA3 overexpression was correlated with the tumor (T) stage and that the expression of all three SKA genes was correlated with the metastasis (M) stage, although no correlation was observed with the nodes (N) stage or patient age (Table). Thus, these results support the potential of SKA complex expression as a biomarker for ACC.

Genes coexpressed with the SKA complex suggest biological functions in ACC

To further evaluate the role of the SKA complex in ACC, we sought to identify coexpressed genes. Our analysis identified a total of 188 genes significantly correlated with SKA1, 1088 with SKA2, and 321 with SKA3 in the TCGA transcriptome database

(absolute correlation >0.7; P value < 0.001). The top 10 genes with positive coexpression and the top 10 genes with negative coex- pression of the SKA complex are shown in heat maps (Fig. 5A-C). In addition, Venn diagrams indicated that the coexpression of 163 genes was correlated with the coexpression of the three SKA subunits in combination (Fig. 5D and Table S2).

For an additional insight into the role of the elevated SKA expression in ACC, we performed GO and KEGG analyses on the 163 coexpressed genes. The results reveal that SKA com- plex coexpressed genes in ACC were enriched in organelle fission, nuclear division, and chromosome segregation path- ways (Fig. 6). We further identified hub genes by a PPI network analysis, which predicted coregulation of the SKA complex with CCNB2, UBE2C, BUB1B, TPX2, CCNA2, CDCA8, CCNB1, MELK, TOP2A, and KIF2C (Table S3 and Fig. S2). Each of these genes was verified to be overexpressed with the SKA subunit genes in ACC. To investigate the association between mRNA expression levels of SKAs and TP53 mutation, we evaluated

Table - Clinicopathological characteristics of adrenocortical carcinoma (ACC) patients from the TCGA database.
CharacteristicLow SKA1High SKA1PLow SKA2High SKA2PLow SKA3High SKA3P
N394039403940
T stage, n (%)0.0310.1140.008
T16 (7.8%)3 (3.9%)6 (7.8%)3 (3.9%)6 (7.8%)3 (3.9%)
T225 (32.5%)17 (22.1%)24 (31.2%)18 (23.4%)26 (33.8%)16 (20.8%)
T33 (3.9%)5 (6.5%)3 (3.9%)5 (6.5%)4 (5.2%)4 (5.2%)
T44 (5.2%)14 (18.2%)5 (6.5%)13 (16.9%)3 (3.9%)15 (19.5%)
N stage, n (%)0.1540.1540.087
N036 (46.8%)32 (41.6%)36 (46.8%)32 (41.6%)37 (48.1%)31 (40.3%)
N12 (2.6%)7 (9.1%)2 (2.6%)7 (9.1%)2 (2.6%)7 (9.1%)
M stage, n (%)0.0250.0250.018
M035 (45.5%)27 (35.1%)35 (45.5%)27 (35.1%)36 (46.8%)26 (33.8%)
M13 (3.9%)12 (15.6%)3 (3.9%)12 (15.6%)3 (3.9%)12 (15.6%)
Age, mean ± SD43.87 ± 15.1849.45 ± 16.040.11746.64 ± 14.6146.75 ± 17.020.97646.13 ± 16.0247.25 ± 15.710.754
Fig. 5 - Identification of genes co-expressed with the spindle and kinetochore-associated (SKA) complex. Expression patterns from The Cancer Genome Atlas (TCGA) database are shown for the top 10 upregulated and the top 10 downregulated genes correlated with the expression of SKA1 (A), SKA2 (B), and SKA3 (C) in adrenocortical carcinoma (ACC). The intersection of co-expression patterns identifies 163 genes co-expressed with the SKA complex (D). The threshold values are |r| > 0.7 and P value < 0.001.

A

8

SKA1

Log2 (TPM+1)

B

Log2 (TPM+1)

6

6

5

SKA2

4

Low

4

Low

High

3

High

2

2

1

0

0

SGO1

KPNA2

NUF2


FEN1


CDCA5


MCM6


CKAP2L


MCM3


EME1


NCAPH


SPAG5


TYMS


ASF1B


CDCA5

BIRC5

AURKA


KIF15


CNOT9


MYBL2


PRC1

MT-CO1

MT-ATP6


MTCO1P12


MT-ND4


MT-ND4

MT-CO1

MT-ND5

MTATP8P1

MT-ND4L


MT-ND4L

MT-ATP8

MT-CO3

MT-ATP6

MT-ATP8

MTATP8P1


MTND4P35

MT-CYB

MT-CYB

MTCO2P12

MT-ND5

Z-score

-2

0

2

Z-score

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-4

-2

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SKA3 Log2 (TPM+1)

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Low

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High

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NUF2

CDC45

D

BRCA2

SKA1


CDCA8


CKAP2L

BUB1B

4

KIF4A


DEPDC1


1

20

BIRC5


RAD51

163


MT-CO1

MT-ND4

839

85

53

MTATP8P1

MTND4P35

MT-ATP6

SKA2

SKA3

MT-CYB

MTCO1P2

MT-CO2

MT-ND5

MTCO1P12

Z-score

-4

-2

0

2

Fig. 6 - Gene ontology (GO) and Kyoto Encyclopedia of Genes and Genome (KEGG) analyses of genes co-expressed with the spindle and kinetochore-associated (SKA) complex in adrenocortical carcinoma (ACC). GO categories for biological processes (BP), cellular composition (CC), and molecular functions (MF); and KEGG pathways (KEGG) are shown for genes correlated with SKA1 (A), SKA2 (B), SKA3 (C), and the intersection at all three subunits of the SKA complex (D).

A

B

Organelle Fission

Chromosome Segregation

Nuclear Division

BP

Nuclear Chromosome

Segregation

BP

Chromosome Segregation

Sister Chromatid

Segregation

Chromosomal Region

Chromosomal Region

Condensed Chromosome

CC

Spindle

CC

Chromosome, Centromeric

Chromosome, Centromeric

Region

Region

Catalytic Activity, Acting on DNA

Catalytic Activity, Acting on DNA

DNA Helicase Activity

MF

Single-Stranded DNA

Binding

MF

DNA-Dependent ATPase

DNA Replication Origin

Activity

Binding

Cell Cycle

KEGG

Cell Cycle

DNA Replication

Spliceosome

KEGG

Fanconi Anemia Pathway

DNA Replication

C

0.05

0.10

0.15

0.20

0.02

0.04

0.06

0.08

0.10

0.12

0.14

0.16

GeneRatio

D

GeneRatio

Organelle Fission

Organelle Fission

Nuclear Division

0

Nuclear Division

BP

Chromosome Segregation

Chromosome Segregation

Chromosomal Region

Chromosomal Region

Condensed Chromosome

CC

Condensed Chromosome

CC

Chromosome, Centromeric

Region

Chromosome, Centromeric

Region

Catalytic Activity, Acting on DNA

Catalytic Activity, Acting on DNA

DNA Helicase Activity

MF

DNA Helicase Activity

MF

DNA-Dependent ATPase

Activity

3’-5’ DNA Helicase

Activity

Cell Cycle

KEGG

Cell Cycle

DNA Replication

Fanconi Anemia Pathway

KEGG

Fanconi Anemia Pathway

DNA Replication

0.05

0.10

0.15

0.20

0.05

0.10

0.15

0.20

0.25

0.30

0.35

0.40

GeneRatio

GeneRatio

the correlation between them in ACC (Figs. S3 and S4). To evaluate the predictive value of changed hub-gene expression in ACC, we performed a ROC analysis (Fig. 7). Our findings provide additional understanding of the mechanisms of ACC and suggest an approach for biomarker discovery using pub- licly available resources.

Discussion

The SKA complex mediates binding to microtubules,25 with an essential role in the progression from metaphase to anaphase.25,26 Recent evidence indicates, however, that the SKA1, SKA2, and SKA3 genes are associated with apoptosis

and have roles in tumor development.12,24,27 Knockdown of SKA1 inhibits migration and invasion,11,28 and SKA2 and SKA3 have been shown to promote proliferation and invasion in various types of cancers.13,27,29 Furthermore, the over- expression of SKA genes has been associated with clinical stage and lymph node metastasis.27 As found in HCC,30 the SKA complex is significantly associated with TP53 mutation status. In our study, we observed an association between SKA complex and TP53 mutation status in ACC (Figs. S3 and S4). Although the potential clinical value of the SKA complex has been reported in other cancers,11,24,27 its role in rare malig- nancies, such as ACC, has not been elucidated.

Notably, we demonstrated that all three SKA subunits are upregulated in ACC and that a high expression of the

Fig. 7 - Receiver Operator Characteristic (ROC) analyses of evaluating the diagnostic values of 10 hub genes in adrenocortical carcinoma (ACC). AUC = area under curve; FPR = false positive rate; TPR = true positive rate.

1.0

0.8

0.6

Sensitivity (TPR)

0.4

0.2

CCNB2 (AUC = 0.821)

UBE2C (AUC = 0.902)

BUB1B (AUC = 0.778)

- TPX2 (AUC = 0.912)

CCNA2 (AUC = 0.761)

- CDCA8 (AUC = 0.789)

- CCNB1 (AUC = 0.893)

- MELK (AUC = 0.855)

- TOP2A (AUC = 0.858)

- KIF2C (AUC = 0.758)

0.0

0.0

0.2

0.4

0.6

0.8

1.0

1-Specificity (FPR)

SKA genes is correlated with overall survival of ACC pa- tients, suggesting predictive potential of the SKA complex as a novel biomarker for ACC. Furthermore, expression was correlated with tumor, nodes, and metastases staging to different extents for the three subunits. To our knowledge, this is the first demonstration of the potential value of the SKA complex as a poor prognostic biomarker and potential therapeutic target for ACC patients. GO and KEGG analysis results demonstrated that genes coexpressed with the SKA

complex were enriched in organelle fission, nuclear divi- sion, and chromosome segregation pathways. In general, errors in chromosome segregation and cell division can lead to aneuploidy, the production of nonviable cells, or the first step in cancer. In addition, a PPI network analysis identified 10 hub genes (CCNB2,31 UBE2C,32 BUB1B,7,33-35 TPX2,36 CCNA2,37 CDCA8,36 CCNB1,38 MELK,36,39 TOP2A,40,41 and KIF2C42), each of which was shown to be dysregulated in ACC. Among them, BUB1B, KIF2C, and TOP2A have been

identified to play important roles in chromosome segrega- tion pathways. 43-45 CCNA2, CCNB1, and MELK are highly associated with cell cycle process. 46-48 Especially, for BUB1B, it has already been identified as a biomarker of aggressive ACC.35 Consistent with the previous findings, our results highlighted the potential value of SKA members as new biomarkers in ACC. Moreover, these findings were consis- tent with the proposed multiple analytic strategy.

Although data for rare malignancies are relatively limited, the SKA complex was found upregulated in ACC patients and high mRNA levels of SKA complex were significantly associ- ated with OS for ACC patients. In the GEPIA database, each of these 10 hub genes was overexpressed and was negatively associated with the prognosis of ACC patients. Therefore, our results are suggestive of a pathway of dysregulation in ACC that involves the SKA complex. Another limitation for the current analyses was the lack of validation in primary speci- mens or cell lines, which could highlight a path to the future.

Interestingly, microRNA-520a-3p (miR-520a-3p) plays an important role as a tumor suppressor gene in the develop- ment and progression of different cancers, and SKA2 is tar- geted by miR-520a-3p in gastric cancer cell lines.49 Therefore, studies to further clarify the role of miR520a-3p and other microRNAs in regulating SKA function in ACC would be of interest. Furthermore, future ablation studies and further investigation to extend our findings to other rare cancers may provide an increased understanding of the role of the SKA complex in different pathways of carcinogenesis.

Previous studies have shown that different SKA members are significantly recognized in different cancers.9-11,13 SKA1 was related to alpha fetoprotein (AFP), tumor size, and tumor, nodes, and metastases staging of liver cancer patients and proliferation, clinical staging, and lymph node metastasis of non-small cell lung cancer patients. While in breast cancer patients, SKA2 was identified to be related to the proliferation, migration, and invasion of cancer cells. The member SKA3 is related to the proliferation and migration of cancer cells and tumor growth in patients with cervical cancer. ACC is a cancer that is highly mutated with major changes in gene copy numbers.5º Combined with our previous results (Fig. 5D), more genes are related to SKA2, whereas less genes are related to SKA1 and SKA3. This could indicate that SKA2 is a better prognostic biomarker for ACC patients.

In summary, our results demonstrate that the mRNA level of the SKA complex is significantly upregulated in ACC. Moreover, the overexpression of SKA1, SKA2, and SKA3 is significantly associated with poor prognosis of ACC patients. These results suggest that the SKA complex has the potential to serve as a poor prognostic biomarker and therapeutic target for ACC patients. Evaluation of SKA proteins in combination with other biomarkers may enhance our understanding of the molecular basis of ACC and help investigators develop new therapies for ACC.

Supplementary Materials

Supplementary data related to this article can be found at https://doi.org/10.1016/j.jss.2022.03.022.

Author Contributions

Shoukai Yu and Jun Ma conceived the study, carried out sta- tistical analysis, wrote, and approved the manuscript.

Acknowledgments

I thank numerous investigators who contributed datasets used here and members of the Lemos laboratory for discus- sions at Harvard University.

Disclosure

None declared.

Funding

This work was supported by the Shanghai Municipal Human Resource Bureau and Shanghai Science and Technology Com- mittee [Pujiang Talent Program grant numbers, 19PJC085].

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