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Identification of EFNA3 as candidate prognosis marker and potential therapeutic target for adrenocortical carcinoma

YANGHAO TAI1, XINZHE LIU1, YIFAN ZHOU1 and JIWEN SHANG1,2

“Department of Urology, Third Hospital of Shanxi Medical University, Shanxi Bethune Hospital, Shanxi Academy of Medical Sciences, Tongji Shanxi Hospital, Taiyuan, Shanxi 030032, P.R. China; 2Department of Urology, Shanxi Bethune Hospital, Shanxi Academy of Medical Sciences, Tongji Shanxi Hospital, Third Hospital of Shanxi Medical University, Taiyuan, Shanxi 030032, P.R. China

Received June 18, 2025; Accepted September 18, 2025

DOI: 10.3892/ol.2025.15346

Abstract. Adrenocortical carcinoma (ACC) is a rare, but highly aggressive endocrine malignancy with poor prognosis and limited treatment options. Identifying novel biomarkers and therapeutic targets is essential for improving patient outcomes. The present study aimed to systematically characterize ephrin-A3 (EFNA3) expression patterns, its prognostic and diagnostic value, and its functional role in ACC progression through multi-omics bioinformatics and in vitro validation. Transcriptomic, epigenetic and pharmacoge- nomic data were obtained from The Cancer Genome Atlas, Genotype-Tissue Expression, Genomics of Drug Sensitivity in Cancer, Cancer Therapeutics Response Portal and MethSurv databases. Expression, survival, immune infiltration, methyla- tion and drug sensitivity analyses were conducted using the R software and online tools (GEPIA2, CIBERSORT and cBio- Portal). competitive endogenous RNA (ceRNA) networks were constructed based on microRNA (miRNA)/long non-coding RNA (lncRNA) predictions. Functional assays, including CCK-8, flow cytometry, Transwell assays were performed on the ACC cell lines, SW-13 and NCI-H295R, to validate EFNA3 function. EFNA3 was significantly upregulated in numerous types of cancer and associated with poor prognosis. In ACC, upregulated EFNA3 was associated with a poor prognosis [Overall survival (OS), hazard ratio (HR)=3.14, 95% CI, 1.49-7.81; disease-specific survival, HR=4.27, 95% CI, 1.70-10.72; progression-free interval, HR=6.24, 95% CI, 2.94-13.23; P<0.05] and diagnostic efficiency (area under the curve=0.829, 95% CI, 0.760-0.897). EFNA3-mutated cases

Correspondence to: Professor Jiwen Shang, Department of Urology, Shanxi Bethune Hospital, Shanxi Academy of Medical Sciences, Tongji Shanxi Hospital, Third Hospital of Shanxi Medical University, 99 Longcheng Street, Xiaodian, Taiyuan, Shanxi 030032, P.R. China E-mail: shangjiwen@sxbqeh.com.cn

Key words: ephrin-A3, adrenocortical carcinoma, pan-cancer analysis, Wnt/ß-catenin signaling, competitive endogenous RNA regulatory network, drug repurposing

had significantly worse OS in ACC specifically (OS, HR=2.97, 95% CI, 1.12-7.90, P=0.029; disease-free survival, HR=8.65, 95% CI, 2.14-34.93, P=0.002). ß-catenin (CTNNB1) was among most frequently co-mutated genes ACC with EFNA3 (P=4.6x10-4). Genetic amplification and DNA methylation alterations were observed in the ACC cohort. EFNA3 expression negatively correlated with immune infiltration and positively correlated with several m6A/m5C regulators. ceRNA network analysis demonstrated key IncRNA-miRNA-EFNA3 axes. Drug sensitivity profiling indicated that EFNA3 expression was associated with statin and proteasome inhibitor responses. The co-expression of positively correlated gene enrichment results suggested that Wnt signaling pathway and ß-catenin/ T-cell factor complex may be involved in the progression of ACC mediated by EFNA3. Functionally, EFNA3 promoted ACC cell proliferation and migration in vitro. The present study demonstrated that EFNA3 acts as an oncogene in ACC and may contribute to tumor aggressiveness via ß-catenin acti- vation and glycolytic reprogramming, and thus may serve as a potential biomarker for prognosis, immunotherapy sensitivity and drug repurposing, particularly involving statins.

Introduction

Adrenocortical carcinoma (ACC) is a rare and highly aggres- sive malignancy arising from steroidogenic cells of the adrenal cortex, characterized by a 5-year overall survival rate of >35% (1). Radical surgical resection remains the only curative approach for localized ACC; however, postoperative recurrence rates are high, ranging between 70-80% (2). For advanced or metastatic ACC, therapeutic options are limited. Mitotane, the only Food and Drug Administration (FDA)-approved agent, demonstrates suboptimal efficacy and substantial toxicity (3). Combination chemotherapy regimens such as mitotane with etoposide, doxorubicin and cisplatin yields modest clinical benefit, with an objective response rate of ~30% and a median progression-free survival of 5.6 months (4). These limita- tions underscore an urgent need to elucidate the molecular mechanisms underlying ACC progression and to identify robust biomarkers for early diagnosis, risk stratification and development of targeted therapeutics.

Reprogramming of cancer cell metabolism is a hallmark of malignancy, with aerobic glycolysis (‘Warburg effect’)

facilitating increased glucose uptake and lactate production, which acidifies the tumor microenvironment (TME) and supports migration and immune evasion (5-7). Dysregulated expression and activity of glycolytic enzymes are central to this phenotype (8). Ephrin-A3 (EFNA3), a transmembrane ligand of the Eph receptor tyrosine kinase family, has been impli- cated in metabolic regulation and tumor progression (9,10). EFNA3 participates in bidirectional cell-cell communication through interactions with Eph receptors, modulating processes such as angiogenesis, cellular motility and tissue remod- eling (11). Notably, EFNA3 functions as a glycolysis-related gene. Previous studies indicate that EFNA3 upregulation promotes glycolytic flux and proliferation in lung adeno- carcinoma, correlating with unfavorable prognosis (12-14), suggesting potential roles as both a metabolic regulator and oncogenic driver.

Members of the EFNA gene family, including EFNA1 and EFNA2, exhibit distinct expression and functional profiles across tumor types. EFNA1 is frequently upregu- lated in various types of cancer, such as gastric cancer and melanomas, and is linked to angiogenesis, immune modula- tion and metastatic potential via interactions with EphA2 and hypoxia-inducible signaling (15-18). Conversely, EFNA2 expression is reduced in certain types of cancer such as gastric carcinoma, with inverse associations to CD8+ T-cell and dendritic cell infiltration, implicating it in immune surveillance escape (19-21). High EFNA3 expression levels are predictive of poorer survival in gastric cancer and correlate negatively with infiltration of B cells, T cells and dendritic cells, as well as with immune checkpoint activity, which indicates a role in immune evasion (22,23). Beyond its prognostic role, EFNA3 expression has been correlated with immune cell infiltration and chemotherapeutic response, indicating potential relevance to tumor immunology and therapeutic resistance (24-26).

The present study aimed to perform an integrative pan-cancer analysis of EFNA3 to evaluate its transcriptional deregulation, genetic and epigenetic alterations, prognostic relevance, associations with tumor immune infiltration and drug sensitivity, and to construct an EFNA3 ceRNA regulatory network. Furthermore, the present study aimed to investigate the effects of EFNA3 on the proliferative, migratory and anti-apoptotic capacities of ACC cells via in vitro experiments.

Materials and methods

Pan-cancer expression profiling of EFNA3. Transcriptome data from 15,776 samples were retrieved via the UCSC Xena Browser (https://xenabrowser.net; The Regents of the University of California), integrating The Cancer Genome Atlas (TCGA) (https://portal.gdc.cancer.gov/) and Genotype-Tissue Expression databases (https://www. gtexportal.org/home/). Raw RNA-Seq data (TPM+1) were log-transformed and normalized using the rms package in R (version 4.2.1; Posit Software, PBC). Batch-corrected data were visualized using ggplot2 (version 3.4.0; Posit Software, PBC) as boxplots to depict EFNA3 expression across tumor and normal tissues. Differential expression was analyzed with DESeq2 (version 1.38.3; Bioconducter), using thresholds of llog2FCI≥1 and FDR ≤0.05 (Benjamini-Hochberg correc- tion). Tumor stage association was analyzed using the ‘Stage

Plot’ module in GEPIA2 (http://gepia2.cancer-pku.cn/). The flowchart of the present study is shown in Fig. S1.

Prognostic and diagnostic evaluation of EFNA3. TCGA clinical and expression datasets were used to assess prognostic and diagnostic relevance of EFNA3. Univariate Cox propor- tional hazards models were constructed using the survival package (version 3.5-5; Posit Software, PBC), with calculated hazard ratios (HR) and 95% confidence intervals (CI). P<0.05 was considered to indicate a statistically significant difference. Samples lacking complete survival data were excluded. Kaplan-Meier survival curves for OS, disease-free survival (DFS) and progression-free interval (PFI) were plotted using survminer (version 0.4.9; Posit Software, PBC) and ggplot2 (version 3.4.0; Posit Software, PBC). Diagnostic value was evaluated using ROC curves generated by the pROC package (version 1.18.0; Posit Software, PBC).

Clinicopathological correlation in ACC. Based on median the expression level of EFNA3, patients with ACC were stratified into high- and low-EFNA3 expression groups (n=40 and n=39, respectively). Clinical parameters were compared using appropriate tests using the stats (version 4.2.1) and car (version 3.1.0) R packages (Posit Software, PBC). Visualization was performed with ggplot2 (version 3.4.0; Posit Software, PBC). The diagnostic performance of EFNA3 in ACC was evaluated via ROC analysis (pROC; version 1.18.0; Posit Software, PBC) using TCGA and UCSC-derived datasets.

Somatic mutation and copy number analysis. Mutation data were obtained from cBioPortal (http://www.cbioportal.org) and TCGA. EFNA3 alterations [mutation type, copy number altera- tions (CNAs) and frequency] were analyzed using 2,683 samples from 2,565 patients. Additional ACC-specific data (n=76) were retrieved from the UCSC Xena (https://xenabrowser.net/) and the International Cancer Genome Consortium (https://dcc.icgc.org/) databases. Kaplan-Meier survival analyses were used to assess survival outcomes based on EFNA3 mutation status. Differential mutation profiles in EFNA3-high vs. - low expression groups were also analyzed.

Epigenetic and mRNA modification analysis. DNA meth- ylation profiles for EFNA3 in ACC were obtained from the MethSurv (https://biit.cs.ut.ee/methsurv/) database. mRNA modification regulator correlations including n1-methyladenosine (m1A), 5-methylcytosine (m5C) and n6-methyladenosine (m6A), were analyzed across various types of cancer from TCGA database using the SangerBox software (version 3.0; http://vip.sangerbox.com). Pearson correlation coefficients and significance levels were reported.

Immune cell infiltration analysis. TME scores (stromal, immune and ESTIMATE scores) were computed using the ESTIMATE R package (version 1.0.13; Posit Software, PBC). Immune infiltration profiling was performed using markers from 22 immune cell types provided by the CIBERSORTx website (https://cibersortx.stanford.edu/) (27). Data were visualized as heatmaps using ggplot2 (version 3.4.0; Posit Software, PBC). Spearman’s correlation coefficients were used to assess statistical associations.

SR

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Competitive endogenous RNA (ceRNA) regulatory network construction. Candidate EFNA3-targeting microRNAs (miRNAs) were predicted using PITA (version 1.0; https:// genie.weizmann.ac.il/pubs/mir07/mir07_data.html), miRanda (version 3.3; http://www.microrna.org/) and TargetScan (version 8.0; http://www.targetscan.org/) software. miRNAs with a negative correlation to EFNA3 were prioritized using the StarBase (version 2.0; http://starbase.sysu.edu. cn/). IncRNA-miRNA interactions were derived from miRNet (version 2.0; https://www.mirnet.ca/) and StarBase (version 2.0; http://starbase.sysu.edu.cn/) under the criteria: Species=human; CLIP-Data=yes; and min stringency=5. Venn diagrams were used for intersecting target prediction using ggplot2 (version 3.4.0; Posit Software, PBC), and VennDiagram (version 1.7.3; Posit Software, PBC). Final IncRNA-miRNA-EFNA3 networks were visualized using mulberry plots using ggplot2 (version 3.4.0; Posit Software, PBC) and ggalluvial (version 0.12.3; Posit Software, PBC).

Drug sensitivity and interaction network analysis. Drug sensitivity data were obtained from the GSCALite (http://bioinfo.life.hust.edu.cn/web/GSCALite/) database, which integrates TCGA, Genomics of Drug Sensitivity in Cancer (GDSC) and Cancer Therapeutics Response Portal (CTRP) datasets. EFNA3-associated drug responses were identified based on Pearson correlations analysis with mRNA expression. FDA-approved agents were selected via DrugBank (https://go.drugbank.com/) annotations. Network graphs were generated using graph (version 1.4.1; Posit Software, PBC) and graph (version 2.1.0; Posit Software, PBC) packages.

Functional enrichment of co-expressed genes. Co-expressed genes were identified using LinkedOmics (http://www.linke- domics.org). Functional enrichment was performed using Gene Ontology (GO) and Kyoto Encyclopedia of Genes and Genomes (KEGG) terms via the clusterProfiler (version 4.6.2; Posit Software, PBC) software. Protein-protein interaction (PPI) networks were generated using the STRING database (https://cn.string-db.org/) and visualized using default Benjamini-Hochberg correction for P-values.

Cell lines and culture conditions. The human ACC cell lines SW-13 (hormonally inactive) and NCI-H295R (hormon- ally active) were obtained from Procell Life Science & Technology Co., Ltd. Cell line authentication was confirmed via short tandem repeat profiling. Cells were maintained in DMEM/F12 medium (Shanghai Zhongqiao Xinzhou Biotechnology Co., Ltd.) supplemented with 10% fetal bovine serum (FBS; cat. no. G24-70500; Genial Biologicals, Inc.) and 1% penicillin-streptomycin (Shanghai Zhongqiao Xinzhou Biotechnology Co., Ltd.). Cultures were incubated at 37℃ in a humidified atmosphere containing 5% CO2.

EFNA3 overexpression and knockdown via lentiviral transfection. The EFNA3 overexpression plasmid was synthesized by Shanghai Sangong Pharmaceutical Co., Ltd. The short hairpin RNA (shRNA) targeting EFNA3 and the non-targeting negative control (NC) were synthesized by Shanghai Gema Gene Biotechnology Co., Ltd. Sequences used were as follows: shNC sense (S), 5’-TTCTCCGAACGT

GTCACGT-3’ and anti-sense (AS), 5’-ACGTGACACGTT CGGAGAA-3’; shEFNA3 S, 5’-GGCATGCGGTGTACT GGAACA-3’ and AS, 5’-TGTTCCAGTACACCGCATGCC-3’. The EFNA3 overexpression plasmid was designed and synthesized by Shanghai Sangong Pharmaceutical Co., Ltd., and constructed by cloning the EFNA3 coding sequence into the pcDNA3.1 plasmid backbone (Thermo Fisher Scientific, Inc.). For transfection, 2.5 µg of plasmid DNA was complexed using Lipofectamine® 2000 (Thermo Fisher Scientific, Inc.) according to the manufacturer’s instructions and then added to the cell culture. Transfection was performed at 37℃ for 48 h. Upon reaching 30-40% confluency in 6-well plates, cells were infected with lentivirus in medium containing Polybrene (Thermo Fisher Scientific, Inc.). Puromycin (4 µg/ml; Thermo Fisher Scientific, Inc.) was added 48 h post-infection for initial screening. Stable-transfected clones were maintained in a 2 µg/ml-puromycin environment.

Real-time quantitative PCR (RT-qPCR). According to the manufacturer’s protocol, total RNA was isolated from NCI-H295R and SW-13 cells using TRIzol reagent (cat. no. R0016; Biocytogen). cDNA was synthesized from mRNA using a cDNA reverse transcription kit (cat. no.4368814; Thermo Fisher Scientific, Inc.) according to the manufacturer’s protocol. qPCR amplification was performed using the SYBR Green fluorescent quantitative PCR kit (cat. no. A46012, Thermo Fisher Scientific, Inc.). The primer sequences are as follows: EFNA3 forward (F), 5’-ATGAAGGTGTTCGTC TGCT-3’ and reverse (R), 5’-CTCAAAGTCTTCCAGCAC G-3’; GAPDH F, 5’-TCAAGATCATCAGCAATGCC-3’ and R, 5’-CGATACCAAAGTTGTCATGGA-3’; GAPDH was used as the internal reference gene. The relative expression level of EFNA3 mRNA was calculated using the 2-44Cq method (28). The thermocycling conditions were as follows: Initial denatur- ation at 95℃ for 10 min; followed by 40 cycles of denaturation at 95℃ for 15 sec and combined annealing/extension at 60℃ for 60 sec.

Transwell migration assay. Cell migration was assessed using 24-well Transwell chambers with 8-um pore inserts (Corning, Inc.). After serum starvation for 24 h, cells were harvested and resuspended in serum-free DMEM at 1x105 cells/ml. Then, 200 ul of cell suspension was seeded into the upper chamber. The lower chamber contained 600 ul of DMEM supplemented with 10% FBS as chemoattractant. After 48 h of incubation at 37℃ with 5% CO2, non-migrated cells were removed. Migrated cells were fixed with 4% paraformaldehyde for 10 min and stained with 0.1% crystal violet for 20 min, both at room temperature. Cell images were captured using an inverted fluorescence microscope (Olympus IX73; Olympus Corporation; magnification, x400). Representative scale bars (200 um) are shown. Each experiment was performed in triplicate and repeated three times independently.

Cell proliferation assay. Cell proliferation was assessed using the Cell Counting Kit-8 (CCK-8; Beyotime Institute of Biotechnology). Cells were seeded in 96-well plates (2,000 cells/well) in 100 ul of complete medium. At 12, 24, 48 and 72 h post-seeding, the medium was replaced with 90 ul of serum-free medium with 10 ul of CCK-8 solution,

followed by 1 h incubation at 37℃. Absorbance was measured at 450 nm using a microplate reader. Each cell experiment was independently repeated three times.

Apoptosis assay. Apoptosis was quantified using Annexin V-FITC/propidium iodide (PI) Apoptosis Detection Kit (BD Biosciences). Transfected cells were seeded into 6-well plates and cultured to ~80% confluence. Cells were harvested, washed twice with PBS and stained in binding buffer with Annexin V-FITC and PI for 10 min at room temperature in the dark. Samples were analyzed within 1 h using flow cytometry (BD FACSCalibur™M; BD Biosciences) and apoptotic populations were quantified. The total apoptosis rate was defined as the sum of early and late apoptotic populations. Data were analyzed using FlowJo software (version 10.8.1; BD Biosciences). Each cell experiment was independently repeated three times.

Cell cycle analysis. Cell cycle analysis was performed using PI staining to quantify DNA content and analyzed via flow cytom- etry. Cells from different groups were collected and washed with ice-cold PBS. After centrifugation at 500 x g for 5 min and aspiration of the supernatant, the cell pellets were fixed in 1 ml of ice-cold 70% ethanol overnight at 4℃. Following PBS washes three times for 5 min each at room temperature with centrifugation at 500 x g for 5 min per wash, cells were incubated in PI/RNase Staining Buffer (BD Biosciences) for 30 min at 37℃ in the dark. Finally, the stained cells were analyzed using a flow cytometer (BD FACSCalibur™M; BD Biosciences). Data were interpreted using the CellQuest Pro software (version 6.0; BD Biosciences). Each cell experiment was independently repeated three times.

Wound healing assay. Cell migration was assessed using a wound healing assay in two human ACC cell lines, SW-13 and NCI-H295R. Cells were harvested during the loga- rithmic growth phase, trypsinized and seeded uniformly into 6-well plates. The cells were cultured until >90% confluence was reached. Prior to wounding, cells were serum-starved in serum-free DMEM for 24 h. A straight wound was introduced in the center area using a sterile pipette tip. The detached cells were removed by washing three times with PBS. Subsequently, serum-free cell culture medium was added. Wound images were captured at 0 and 48 h under an inverted fluorescence microscope (Olympus IX73; Olympus Corporation; magnification, x40). The same magnifica- tion and fields of view were used for each time point. Representative scale bars (500 um) are shown on respective images. The measurement of wound width was performed by annotating the wound edges on the images. Migration rates were quantified using ImageJ (version 1.8.0; National Institutes of Health) and calculated as follows: Cell migra- tion rate=(scratch width at 0 h-scratch width at 48 h)/scratch width at 0 h x100). Each cell experiment was independently repeated three times.

Statistical analysis. All statistical analyses were performed using R (version 4.2.1; Posit Software, PBC). Quantitative data are expressed as mean ± standard deviation. For the compari- sons in Fig. 1, the Wilcoxon rank-sum test (Mann-Whitney U test) was used for unpaired samples, while the Wilcoxon

signed-rank test was applied for paired samples. For in vitro comparisons, unpaired Student’s t-test was used for two-group analyses. For comparisons involving ≥3 groups, data were assessed for normality and homogeneity of vari- ances. The normality of data distribution was verified using the Shapiro-Wilk test, and the homogeneity of variances was assessed using Levene’s test. If these assumptions were met, one-way ANOVA was performed, followed by Tukey’s post hoc test for pairwise comparisons. If the assumptions were violated, the Kruskal-Wallis test was used, followed by Dunn’s post hoc test. The categorical variables were compared using the x2 test. When the applicable conditions of the x2 test were violated (>20% of the expected frequency is <5) the Fisher exact test was used instead. P<0.05 was considered to indicate a statistically significant difference.

Results

EFNA3 expression patterns and prognostic relevance across various types of human cancer. The differential expression of EFNA3 was assessed in a pan-cancer analysis by comparing normal tissues from the GTEx database against tumor tissues from the TCGA dataset. EFNA3 expression levels were signif- icantly downregulated in glioblastoma multiforme (GBM), kidney chromophobe (KICH), acute myeloid leukemia-like (LAML) and skin cutaneous melanoma (SKCM) compared with that of normal tissues (Fig. 1A). Pan-cancer analysis using the TCGA data of paired tumor and paracancerous tissues from the same patients demonstrated that EFNA3 expression levels were significantly upregulated in the majority of tumor types compared with that of paired paracancerous tissues; however, significant downregulation was observed in GBM, KICH, LAML and SKCM (Fig. 1B). The expression levels of EFNA3 in cancer and normal tissues in various types of cancer are shown in Tables SI-III. Forest plots generated from Cox proportional hazard models demonstrated that EFNA3 expression was significantly associated with OS (Fig. 2A), disease-specific survival (DSS; Fig. 2B) and PFI (Fig. 2C) across various cancer types.

Prognostic and pathological correlations of EFNA3 in pan-cancer analysis. Survival data from TCGA were used to assess the prognostic role of EFNA3. The association of EFNA3 expression levels with survival events and time in various cancer types are shown in Table SIV-VI. Due to incom- plete survival annotations, certain end points, specifically DSS and PFI, were unavailable for LAML. Univariate Cox regres- sion showed that increased EFNA3 expression was associated with poor OS, DSS and PFI in bladder cancer (BLCA), kidney clear cell carcinoma (KIRP), ACC and mesothelioma (HR>1; P<0.05). By contrast, increased EFNA3 expression conferred a protective role in lower-grade glioma (LGG; HR<1; P<0.05; Fig. 2). EFNA3 was an adverse marker for PFI in breast cancer (BC), esophageal carcinoma (ESCA), prostate adenocarci- noma (PRAD), rectum adenocarcinoma (READ) and cervical endocervical squamous carcinoma (CESC), and for DSS in liver hepatocellular carcinoma (LIHC), SKCM and CESC (Figs. 3 and S2). Specifically, the Kaplan-Meier survival anal- ysis and log-rank testing demonstrated that, compared to those in the EFNA3-low expression group, high EFNA3 expression

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Figure 1. EFNA3 expression levels and prognosis in various types of cancer. (A) Differences in EFNA3 expression between various types of cancer and normal tissues in TCGA + GTEx. The error bars indicate the standard deviation. The Wilcoxon rank-sum test was used for analysis of unpaired samples. (B) Pairwise difference analysis of EFNA3 expression between tumors and adjacent normal tissues. The Wilcoxon signed-rank test was used for paired samples. "P<0.05, ** P<0.01 and *** P<0.001. EFNA3, ephrin-A3; ACC, adrenocortical carcinoma; ns, no significance.

A

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Expression of EFNA3 Log2 (TPM+1)

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Normal

A

M

Tumor

2

0

0

ACC

BLCA

BC

CESC

CHOL

COAD

DLBC

ESCA

GBM

HNSC

KICH

KIRC

KIRP

LAML

LGG

LIHC

LUAD

LUSC

MESO

OV

PAAD

PCPG

PRAD

READ

SARC

SKCM

STAD

TGCT

THCA

THYM

UCEC

UCS

UVM

B

:

ns

:


Expression of EFNA3 Log2 (TPM+1)


9


ns

ns




ns


ns


ns


4

Normal

Tumor

ns

2


0

BLCA

BC

CESC

CHOL

COAD

ESCA

HNSC

KICH

KIRC

KIRP

LIHC

LUAD

LUSC

PAAD

PCPG

PRAD

READ

SARC

SKCM

STAD

THCA

THYM

UCEC

A

EFNA3 - OS

B

GroupTotal (N)HR (95% CI)P-value
ACC793.412 (1.491 - 7.806)0.0037
BLCA4111.445 (1.077 - 1.939)U 0.0140
BC10861.139 (0.828 - 1.569)0.4237
CESC3061.629 (1.017 - 2.610)1 0.0424
CHOL352.071 (0.773 - 5.553)0.1479
COAD4771.247 (0.845 - 1.839)0.2663
DLBC480.939 (0.234 - 3.768)0.9290
ESCA1630.689 (0.420 - 1.130)0.1399
GBM1681.009 (0.718 - 1.416)0.9609
HNSC5031.098 (0.841 - 1.433)0.4924
KICH641.164 (0.312 - 4.336)0.8211
KIRC5411.431 (1.061 - 1.931)0.0189
KIRP2901.156 (0.637 - 2.097)0.6345
LAML1390.985 (0.645 - 1.505)0.9457
LGG5300.674 (0.480 - 0.945)0.0224
LIHC3731.700 (1.198 - 2.411)0.0029
LUAD5301.273 (0.955 - 1.698)0.1000
LUSC4960.779 (0.594 - 1.022)0.0713
MESO862.156 (1.317 - 3.528)0.0022
OV3790.895 (0.692 - 1.158)0.3993
PAAD1791.286 (0.854 - 1.936)0.2289
PCPG1840.960 (0.239 - 3.854)0.9543
PRAD5010.622 (0.159 - 2.431)0.4949
READ1661.803 (0.816 - 3.982)0.1450
SARC2631.528 (1.025 - 2.278)0.0375
SKCM4571.407 (1.075 - 1.842)0.0128
STAD3700.755 (0.544 - 1.048)0.0929
TGCT1390.349 (0.036 - 3.357)0.3621
THCA5120.883 (0.331 - 2.354)0.8040
THYM1190.605 (0.149 - 2.458)0.4819
UCEC5531.469 (0.972 - 2.220)0.0678
UCS570.834 (0.421 - 1.654)0.6037
UVM805.756 (2.107 - 15.724)I 0.0006

EFNA3 - DSS

GroupTotal (N)HR (95% CI)P-value
ACC774.272 (1.703 - 10.718)0.0020
BLCA3971.524 (1.068 - 2.174)0.0203
BC10661.707 (1.097 - 2.655)0.0178
CESC3021.781 (1.034 - 3.069)0.0376
CHOL341.768 (0.629 - 4.968)0.2795
COAD4611.319 (0.804 - 2.162)N 0.2727
DLBC480.315 (0.033 - 3.030)0.3173
ESCA1620.616 (0.341 - 1.113)0.1084
GBM1550.965 (0.673 - 1.383)0.8447
HNSC4781.116 (0.790 - 1.578)0.5326
KICH641.229 (0.275 - 5.493)0.7876
KIRC5301.786 (1.212 - 2.632)- 0.0034
KIRP2861.594 (0.746 - 3.404)0.2288
LGG5220.685 (0.480 - 0.978)0.0375
LIHC3651.433 (0.920 - 2.231)0.1111
LUAD4951.128 (0.785 - 1.621)0.5149
LUSC4440.852 (0.559 - 1.299)0.4561
MESO662.792 (1.460 - 5.341)0.0019
OV3530.877 (0.664 - 1.158)0.3538
PAAD1731.243 (0.784 - 1.968)H 0.3550
PCPG1840.935 (0.188 - 4.660)0.9351
PRAD4993.047 (0.326 - 28.457)0.3283
READ1602.283 (0.760 - 6.853)0.1411
SARC2571.606 (1.032 - 2.499)0.0357
SKCM4511.437 (1.078 - 1.915)0.0134
STAD3490.766 (0.505 - 1.162)0.2095
TGCT1390.532 (0.048 - 5.868)0.6063
THCA5060.676 (0.151 - 3.024)0.6089
THYM1191.263 (0.173 - 9.214)0.8179
UCEC5511.301 (0.790 - 2.142)0.3019
UCS550.890 (0.435 - 1.822)0.7498
UVM806.491 (2.161 - 19.495)0.0009

C EFNA3 - PFI

GroupTotal (N)HR (95% CI)P-value
ACC796.237 (2.940 - 13.231)1.84c-06
BLCA4121.481 (1.102 - 1.990}0.0093
BC10861.262 (0.911 - 1.748}0.1617
CESC3061.435 (0.901 - 2.285}0.1279
CHOL351.119 (0.464 - 2.699]0.8021
COAD4771.287 (0.909 - 1.823]N 0.1554
DLBC480.742 (0.224 - 2.455}0.6246
ESCA1630.625 (0.400 - 0.976)0.0387
GBM1680.817 (0.581 - 1.148}0.2442
HNSC5031.248 (0.939 - 1.658]0.1272
KICH641.136 (0.347 - 3.722}0.8336
KIRC5391.725 (1.255 - 2.372}0.0008
KIRP2891.444 (0.851 - 2.448]0.1728
LGG5300.762 (0.581 - 1.000}0.0501
LIHC3731.300 (0.972 - 1.739]0.0766
LUAD5301.155 (0.888 - 1.502)0.2834
LUSC4970.945 (0.683 - 1.307)0.7318
MESO842.090 (1.214 - 3.598)0.0078
OV3790.935 (0.738 - 1.184)0.5757
PAAD1791.068 (0.728 - 1.567)0.7353
PCPG1842.057 (0.837 - 5.056)0.1160
PRAD5011.540 (1.018 - 2.329)0.0411
READ1661.972 (1.010 - 3.852)0.0467
SARC2631.069 (0.769 - 1.486)0.6913
SKCM4581.118 (0.894 - 1.398)0.3298
STAD3720.736 (0.517 - 1.048)0.0887
TGCT1391.010 (0.542 - 1.883)0.9747
THCA5121.010 (0.592 - 1.723)0.9698
THYM1190.794 (0.331 - 1.905)0.6047
UCEC5531.381 (0.974 - 1.957)0.0701
UCS570.857 (0.445 - 1.651)0.6447
UVM793.298 (1.434 - 7.586)0.0050

0

3

10

8

10

1’5

8

$

10

Figure 2. Forest plots demonstrate the prognostic value of EFNA3 in 33 types of cancer. (A) Forest plot of EFNA3 expression levels versus OS in patients with cancer. (B) Forest plot of EFNA3 expression levels versus DSS in patients with cancer. (C) Forest plot of EFNA3 expression level versus PFI in patients with cancer. Red text represents high expression levels associated with poor prognosis, while green text represents high expression levels associated with good prognosis. Conditional assumptions applied: Observations were independent and the risk ratio does not change over time (proportional risk assumption). The univariate Cox regression test was employed to calculate the HR with 95% CI and to determine the P-value. EFNA3, ephrin-A3; ACC, adrenocortical carcinoma; OS, overall survival; DSS, disease-specific survival; PFI, progression-free interval; HR, hazard ratio.

Figure 3. Prognostic value analysis. Survival curves for ACC, BLCA, KIRC, LGG and MESO in EFNA3-high and -low expression groups. The log-rank test was employed to compare the survival curves and determine the P-value. EFNA3, ephrin-A3; ACC, adrenocortical carcinoma; BLCA, bladder cancer; KIRC, kidney clear cell carcinoma; LGG, lower-grade glioma; MESO, mesothelioma; OS, overall survival; DSS, disease-specific survival; PFI, progression-free interval; HR, hazard ratio.

1.0

EFNA3

1.0

EFNA3

1.00

EFNA3

Low

Low

Low

Survival probability

High

Survival probability

High

Survival probability

High

0.8

0.8

0.75

ACC

#

0.6

0.6

0.50

os

DSS

PFI

0.4

HR=3.41(1.49-7.84)

0.4

HR=4.27(1.70-10.72)

0.25

HR=6.24(2.94-13.23)

P=0.004

+

H

P=0.002

#

P<0.001

#

0

1000

2000

3000

4000

0

1000

2000

3000

4000

0

1000

2000

3000

4000

No. at risk

Time (days)

No. at risk

Time (days)

No. at risk

Time (days)

Low

39

25

15

5

0

Low

37

24

15

5

0

Low

39

21

12

4

0

High

40

21

7

3

2

High

40

21

7

3

2

High

40

7

4

2

2

1.0

EFNA3

1.0

EFNA3

1.00

EFNA3

Low

Low

High

0.9

Low

Survival probability

0.8

Survival probability

High

Survival probability

0.75

High

0.8

BLCA

0.6

0.7

0.50

+

0.6

0.4

OS

DSS

0.25

0.5

+T

PFI

HR=1.45(1.08-1,94)

HR=1.52(1.07-17)

HR=1.48(1.10-1.99)

P=0.014

P=0.020

+

0.4

0.00

P=0.009

0

1000

2000

3000

4000

5000

0

1000

2000

3000

4000

5000

0

1000

2000

3000

4000

5000

No. at risk

Time (days)

No. at risk

Time (days)

No. at risk

Time (days)

Low

206

55

21

4

3

1

Low

202

55

21

4

3

1

Low

206

47

19

3

2

High

205

45

17

8

1

1

High

195

44

17

8

1

1

High

206

32

13

7

1

1.0

EFNA3

1.0

EFNA3

1.0

EFNA3

Low

Low

Low

Survival probability

0.9

High

Survival probability

High

Survival probability

High

0.9

0.8

0.8.

KIRC

0.7

0.8

0.6.

0.6

0.5

os

0.7

DSS

HR=1.43(1.06-1.93)

HR=1.79(1.21-2.63)

0.4.

PFI

HR=1.73(1.25-2.37)

P=0.019

P=0.003

P<0.001

0

1000

2000

3000

4000

0

1000

2000

3000

4000

0

1000

2000

3000

4000

No. at risk

Time (days)

No. at risk

Time (days)

No. at risk

Time (days)

Low

270

161

66

23

2

Low

262

159

64

23

2

Low

268

136

53

16

1

High

271

149

56

17

1

High

268

146

56

17

1

High

271

132

43

12

0

1.00

EFNA3

1.00

EFNA3

1.00

EFNA3

Low

Low

Low

Survival probability

High

Survival probability

High

High

0.75

0.75

Survival probability

0.75

LGG

0.50

0.50

0.50

0.25

os

0.25

DSS

0.25

PFI

HR=0.51(0.40-0.65)

HR=0.50(0.39-0.65)

HR=0.57(0.46-0.71)

+

P<0.001

1

P<0.001

P<0.001

+

+

0.00

0

2000

4000

6000

0

2000

4000

6000

0

1000

2000

3000

4000

5000

No. at risk

Time (days)

No. at risk

Time (days)

No. at risk

Time (days)

Low

348

24

5

0

Low

336

24

5

0

Low

348

48

15

6

3

0

High

350

39

10

1

High

341

37

10

1

High

350

82

19

6

1

1

1.00

EFNA3

1.00

EFNA3

1.00

EFNA3

Low

Low

Low

Survival probability

High

High

High

0.75

Survival probability

Survival probability

0.75

0.75

0.50

0.50

0.50

MESO

0.25

os

0.25

DSS

0.25

PFI

HR=2.16(1.32-3.53)

HR=2.79(1.46-5.34)

HR=2.09(1.21-3.60)

+

0.00

P=0.002

0.00

P=0.002

P=0.008

+

0

1000

2000

0

1000

2000

0

500

1000

1500

2000

No. at risk

Time (days)

No. at risk

Time (days)

No. at risk

Time (days)

Low

42

12

4

Low

32

10

3

Low-

41

19

7

3

1

High

44

2

0

High

34

1

0

High

43

8

0

0

0

SPANDIDOS PUBLICATIONS

.8.

was significantly associated with poorer PFI in PRAD, READ, BC, ESCA and CESC, and poorer DSS in LIHC, SKCM and CESC (Fig. 3). Significant correlations between EFNA3 and pathological stage were present in certain tumors, including ACC, cholangiocarcinoma (CHOL), ESCA, KIRP, LIHC, testicular germ cell tumors, thyroid carcinoma and SKCM (Fig. S3).

Genetic alterations of EFNA3 and their prognostic signifi- cance. Analysis 2,683 samples from a pan-cancer database of 2,565 patients demonstrated that 15% of the cohort harbored EFNA3 alterations (Fig. 4A), with the highest frequency observed in BC (>40%; Fig. 4B). In ACC, the mutation frequency was 8%. CNAs of the ‘mRNA high’ and ‘amplifi- cation’ subtypes occurred most frequently in ACC. EFNA3 CNAs positively correlated with mRNA expression (Fig. 4℃). Differential expression of genes between EFNA3 altered and unaltered groups in ACC are shown in Table SVII. Survival analyses demonstrated that EFNA3-mutated cases had significantly lower OS in the pan-cancer analysis (HR=2.52, 95% CI, 1.45-4.37; P<0.001) and in ACC specifically (OS, HR=2.97, 95% CI, 1.12-7.90, P=0.029; DFS HR=8.65, 95% CI, 2.14-34.93, P=0.002; Fig. 4D-F). In ACC, ß-catenin (CTNNB1) was among the most frequently co-mutated genes with EFNA3 (P=4.6x10-4; Fig. 4G).

DNA methylation and RNA modifications in the epigenetic regulation of EFNA3. The MethSurv software was used to identify 29 CpG methylation sites for EFNA3 in ACC (Fig. 5A and Table SVIII). The expression levels of EFNA3 positively correlated with multiple mRNA methylation regulators including m1A-, m5C- and m6A-related enzymes (Fig. 5B). The correlation and P-values between the expression level of EFNA3 and mRNA methylation regulatory factors are shown in Table SIX and SX. Top regulators included HNRNPC, ALKBH5, NSUN6, HNRNPA2B1, ELAVL1, METTL3, YTHDF2, LRPPRC and ALYREF.

Correlation between EFNA3 expression levels and the immune microenvironment. In ACC, EFNA3 expression was inversely correlated with stromal, immune and ESTIMATE scores (Fig. 6A). Using the CIBERSORT algorithm, EFNA3 expression was significantly associated with the infiltration levels of multiple immune cell subtypes (Fig. 6B), which indicated potential immunomodulatory roles. For instance, in ACC, EFNA3 expression showed the strongest positive corre- lation with the infiltration levels of activated dendritic cells and the strongest negative correlation with M1 macrophages, both of which were statistically significant (P<0.05).

EFNA3 expression and drug sensitivity prediction. were screened CTRP analysis demonstrated a positive correla- tion between EFNA3 expression and sensitivity to lovastatin and fluvastatin, and a negative correlation with austocystin D, ibrutinib and lapatinib (Fig. 7A). In the GDSC dataset, EFNA3 expression levels correlated positively with bort- ezomib, dimethyloxalylglycine and dasatinib sensitivity but negatively with CP-724714, WZ3105 and KIN001-102. Additionally, using a cut-off of FDR<0.05, 24 (CTRP) and 14 (GDSC) FDA-approved antitumor drugs were significantly

associated with EFNA3 expression levels (Fig. 7B and C; Tables SXI and SXII).

Association of EFNA3 with clinicopathological features in ACC. EFNA3 expression levels were significantly associated with primary treatment outcome (P=0.015), Weiss necrosis (P=0.039), tumor status (P<0.001), diffuse architecture (P=0.026), pathological stage (P=0.034), N-stage (P=0.037) and sex (P=0.030; Table I and Fig. 8A-F). Diagnostic ROC analysis demonstrated a high discriminatory power of EFNA3 [area under the curve (AUC)=0.829; Fig. 8G]. The ROC curve analysis demonstrated that EFNA3 exhibited diagnostic accuracy for ACC across multiple time points. The AUC was 0.764 for 1-year survival, 0.756 for 3-year survival and 0.812 for 5-year survival. Furthermore, on the 1-year ROC curve, a cut-off value of 5.526 was identified for EFNA3 expression (Fig. 8H). The time-dependent ROC analysis assessed the trend of EFNA3 diagnostic accuracy over time. The AUC remained at a high level (≥0.7) across all time points (Fig. 8I).

EFNA3 related ceRNA network construction in ACC. The PITA, miRanda and TargetScan databases were used to analyze and predict 85, 30 and 20 EFNA3 target miRNAs, respectively. A total of 12 target miRNAs were found to be in common from the three database predictions, including hsa-miR-30d-5p, hsa-miR-224-5p, hsa-miR-30c-5p, hsa-miR-30a-5p, hsa-miR-30b-5p, hsa-miR-30e-5p, hsa- miR-330-5p, hsa-miR-326, hsa-miR-145-5p, hsa-miR-491-5p, hsa-miR-153-3p and hsa-miR-210-3p (Fig. 9A). In addition, correlation analysis between target miRNAs and EFNA3 expression was performed to identify candidates for further investigation of ceRNA interactions. Correlation analysis demonstrated the expression levels of 6 target miRNAs negatively correlated with EFNA3 expression levels, namely hsa-miR-145-5p (r =- 0.365, P=9.26x10x10-4), hsa-miR-30b-5p (r =- 0.327, P=3.23x10-3), hsa-miR-30a-3p (r =- 0.44, P=5.06x10-5), hsa-miR-30c-5p (r =- 0.343, P=1.95x10-3), hsa-miR-224-5p (r =- 0.281, P=1.20x10-2) and hsa-miR-30d-5p (r =- 0.456, P=2.45x10-5; Fig. 9B). TargetScan was used to predict the potential binding sites of EFNA3 to the target miRNAs identified (Fig. 9C).

The miRNet and starBase online databases were used to further predict lncRNAs that may bind to the six target miRNAs (hsa-miR-145-5p, hsa-miR-30b-5p, hsa-miR-30a-5p, hsa-miR-30c-5p, hsa-miR-224-5p and hsa-miR-30d-5p; Fig. 10A). A negative correlation between specific lncRNAs and miRNA was observed; the ceRNA network hypothesis suggests that the lncRNA may act as a molecular sponge, sequestering the miRNA and reducing its regulatory activity, consistent with miRNA-mediated ceRNA crosstalk (29). Therefore, the starBase database was used to analyze the correlation between target lncRNA expression and miRNA in ACC. Correlation analysis proved that there are 5 target lncRNAs expression levels that are negatively correlated with hsa-miR-30d-5p, namely AC239868.1, EPB41L4A-AS1, AL049840.4, OIP5-AS1 and SNHG16 (Fig. 10B). However, only the expression level of SNHG16 was negatively correlated with hsa-miR-30c-5p (Fig. 10C). Furthermore, the expression of OIP5-AS1 and SNHG16 were negatively correlated with hsa-miR-30b-5p (Fig. 10D). The expression of MAGI2-AS3 and

Figure 4. Analysis of genetic alterations. (A) Genetic alterations of EFNA3 in a pan-cancer database and ACC, accounting for 15% (alteration/analysis= 384/2,565) and 8% (6/67) of the alterations, respectively. (B) Frequency of altered EFNA3 mutation types in different types of cancer. (C) mRNA expression of EFNA3 putative CNAs in pan-cancer tissues and ACC. Proportional risk hypothesis testing was performed using the survival package and fitted survival regressions, and the results were visualized using the survminer package as well as the ggplot2 package. (D) Kaplan-Meier curves of EFNA3 mutation status versus OS in pan-cancer analysis. (E) Kaplan-Meier curves of EFNA3 mutation status and OS in ACC. (F) Kaplan-Meier curves of EFNA3 mutations in ACC versus DFS. (G) The top 2 genes with the highest mutation frequency in the EFNA3-high and -low expression group in ACC. EFNA3, ephrin-A3; ACC, adrenocortical carcinoma; OS, overall survival; DFS, disease-free survival; HR, hazard ratio; CNA, copy number alterations; Del, deletion; MutCount, mutation count; CTNNB1, B-catenin; VUS, variants of uncertain significance.

A

Pan-cancer 15%

Amplification

ACC 8%

Deep deletion

Inframe mutation (unknown significance)

Missense mutation (unknown significance)

mRNA high

No deletion

B

Deep deletion

8%

40%

Multiple alterations

Amplification

6%

Alteration frequency

30%

mRNA high

Mutation

4%

20%

10%

2%

Mutation data

+

+

×

+

+

+

+

+

+

+

+

+

+

+

+

+

+

+

*

+

+

X

+

+

+

+

+

+

CNA data +

X

X

+

+

+

+

+

+

+

+

+

+

+ -

+

+

+

X

+

+

+

+

X

X

+

+

+

+

mRNA data

+

+

+

+

HCC +

LUCA +

BLCA +

UCEC +

+

EC

CRC

CESC

NSCLC

SKCM +

ESCA +

Ov +

HNSC

BC

PAAD

STS -

1

BONE CA

PRAD +

MBCL +

EMBR

KIRC +

-

AML

MB

THCA +

MBCN +

LGG +

+

ET

MDS/MPN

ACC

C

Missense (VUS)

4

Not mutated

13

mRNA expression z-scores relative to all samples (log FPKM capture)

Amplification

O

3

Diploid

12

Shallow deletion

mRNA expression (RNA Seq V2 RSEM)

11

2

O

0

(log2(value+1))

10

9

1

8

0

7

6

-1

5

-2

CESC

MBCN

PTLD

-4

BLCA

BC

CRC

EC

ESCA

LGG

HNSC

HCC

LUCA

MBCL

MEL

NSCLC

OV

PRAD

KIRC

STS

THCA

UCEC

ACC

D

Pan-cancer OS

E

ACC OS

F

ACC DFS

1.00

Unaltered group

1.0

Unaltered group Altered group

1.00

Altered group

5

Unaltered group Altered group

Survival probability

0.75

Survival probability

0.8

Survival probability

0.75

0.50

0.6

0.50

0.25

0.4

0.25

HR=2.52(1.45-4.37)

0.2

HR=2.97(1.12-

.90)

HR=8.65(2.14-34.93)

0.00

P<0.001

P=0.029

0.00

P=0.002

G

0

25

50

75

0

50

100

Time

Time

150

0

50

100

Time

150

2.0

1.5

MutCount

MutCount

1.0

Nonsensev mutation

0.5

Frame shift Del

0.0

Sample group

0

5

10

Missense mutation

Splice site

In frame Del

TP53 (0.06)

56.5%

Frame shift ins

Sample group:

High expression

CTNNB1 (4.6e-4)

52.2%

Low expression

SPANDIDOS PUBLICATIONS

V

8.

Figure 5. Analysis of EFNA3 DNA methylation in adrenocortical carcinoma and pan-cancer expression correlation with mRNA methylation regulators. (A) Heatmap of EFNA3 DNA methylation in ACC from the MethSurv database. (B) Correlation analysis of EFNA3 expression with mRNA modification methylation regulators. Correlation assessed using Pearson's p value and statistical significance. "P<0.05. EFNA3, ephrin-A3; ACC, adrenocortical carcinoma; m1A, n1-methyladenosine; m5C, 5-methylcytosine; m6A, N6-methyladenosine

A

Ethnicity

cg08185345

cg10143807

cg17582777

cg08242010

cg10317026

cg16257681

cg00145979

cg18828883

cg05788417

cg07196758

cg11750116

cg12741345

cg06058618

cg14848832

cg17222196

cg06787675

cg11688696

cg10954985

cg05813084

cg17749735

cg13096820

cg10516701

cg27045062

cg00267713

cg00449821

cg21199495

cg11869514

cg25745642

0.8

Race

Age

Event

0.4

0.4

0.2

Ethnicity

Not evaluted

Unknown

Hispanic or latino

Not hispanic or latino

Race

Not evaluted

Unknown

Asian

Black and afrain american

White

Age

14-34

34-48

48-59

59-77

Event

Alive Dead

Ralation_to_UCSC_CpG

Island

N_Shore

S_Shore

UCSC_RefGene_Group

3’UTR

5’UTR; 1stExon

Body

TSS1500

TSS200

UCSC_RefGene_Group

Ralation_to_UCSC_CpG

B

TRMT61A

TRMT10C

TRMT61B

TRMT6

YTHDF1

YTHDF3

YTHDF2

YTHDC1

ALKBH1

ALKBH3

NSUN7

NSUN6

Correlation coefficient

NSUN3

TRDMT1

NSUN5

-0.5

0.0

0.5

1.0

DNMT1

P-value

NOP2

NSUN2

0.0

0.5

NSUN4

1.0

DNMT3A

DNMT3B

Modification:

TET2

m1A

ALYREF

m5C

KIAA1429

RBM15

m6A

WTAP

RBM15B

Type:

METTL3

Writer

CBLL1

Reader

METTL14

ZC3H13

Eraser

ALKBH5

FTO

YTHDC1_1

YTHDF2_1

HNRNPA2B1

HNRNPC

YTHDF1_1

ELAVL1

FMR1

YTHDC2

YTHDF3_1

IGF2BP1


LBPPRC

TGCT (n=148) SKCM (n=102)

READ (n=92)

GBMLGG (n=662)

LGG (n=509)

HNSC (n=518)

CESC (n=304)

ESCA (n=181)

OV (n=419)

SARC (n=258)

UCS (n=57)

PAAD (n=178)

LUAD (n=513)

LUSC (n=498)

LIHC (n=369)

STAD (n=414)

STES (n=595)

BLCA (n=407)

PRAD (n=495)

CHOL (n=36)

THYM (n=119)

LAML (n=173)

MESO (n=87)

COAD (n=288)

COADREAD (n=380)

BRCA (n=1092)

PCPG (n=177)

KIPAN (n=884)

KIRC (n=530)

NB (n=153)

THCA (n=504)

UCEC (n=180)

ACC (n=77)

WT (n=120)

DLBC (n=47)

GBM (n=153)

ALL (n=132)

KIRP (n=288)

KICH (n=66)

UVM (n=79)

Figure 6. Correlation analysis of EFNA3 expression and immune infiltration. (A) EFNA3 expression level and immune cell infiltration were evaluated based on the ESTIMATE algorithm. (B) EFNA3 expression level and immune cell infiltration were evaluated based on the CIBERSORT algorithm. Correlation assessed using Spearman's p value and statistical significance. * P<0.05. EFNA3, ephrin-A3; Cor, correlation; ns, no significance.

A

Cor

Stromal score

1.0

-0.55

-0.21

-0.13

-0.11

-0.02

-0.09

-0.28

-0.18

-0.40

-0.17

0.18

0.07

-0.11

-0.32

-0.19

-0.26

-0.26

-0.34

-0.31

-0.20

-0.35

0.03

0.01

-0.11

-0.32

-0.24

-0.38

-0.31

-0.06

-0.04

-0.29

-0.34

0.40

0.5

Immune score

-0.64

-0.26

-0.10

-0.09

-0.25

-0.15

-0.55

-0.23

-0.42

-0.36

0.03

0.00

-0.03

-0.20

-0.18

0.01

-0.32

-0.49

-0.47

-0.35

-0.39

0.04

0.00

-0.20

-0.36

-0.28

-0.37

0.12

-0.15

-0.16

-0.35

-0.33

0.49

0.0

ESTIMATE score

-0.64

-0.25

-0.14

-0.13

-0.19

-0.13

-0.51

-0.23

-0.43

-0.31

0.10

0.02

-0.05

0.27

-0.19

0.13

-0.32

-0.45

-0.47

-0.30

-0.40

0.05

0.01

-0.16

-0.37

-0.29

-0.42

-0.07

-0.12

0.18

0.36

-0.37

0.49

-0.1

ACC

BLCA

0 B

CESC

CHOL

COAD

DLBC

ESCA

GBM

HNSC

KICH

KIRC

KIRP

LAML

LGG

LIHC

LUAD

LUSC

MESO

OV

PAAD

PCPG

PRAD

READ

SARC

SKCM

STAD

TGCT

THCA

THYM

UCEC

UCS

UVM

-1.0

B

B cells naive

*

**

* ☒

**

**

* ☒

*

*

**

*

*

B cells memory

*

*

*

*

**

*

*

* ☒

*

Plasma cells

* ☒

*

*

*

* ☒

**

*

*

* ☒

T cells CD8

**

**

*

**

*

**

**

*

T cells CD4 naive

**

T cells CD4 memory resting

**

**

** ☒

*

**

**

**

*

T cells CD4 memory activated


** ☒

**


**


**

**

* ☒

T cells follicular helper


*

*P<0.05



T cells regulatory Tregs

**

** ☒

*

**

**

**

** ☒

*

*

** ☒

**

*

γo T cells

Cor

**

** ☒

**

*

1.0

NK cells resting

*

NK cells activated

0.5

* ☒

* ☒

Monocytes

**

**

**

*

**

**

* ☒

** ☒

0.0

Macrophages MO

*

*

*

*

*

*

*

*

*

**

**

*

*

**

*

*

**

-0.5

Macrophages M1

*

*

*

*

*

*

*

*

*

*

*

*

*

Macrophages M2

-1.0

*

*

*

**

**

*

**

**

**

**

*

Dendritic cells resting

*

*

**

**

*

**

*

*

*

*

*

Dendritic cells activated

*

**

*

*

*

*

*

*

*

Mast cells resting

*

**

**


**

**

**

**

**

*

**

*

Mast cells activated

**


**

**

*

**

**

Eosinophils

*

**

*

*

*

**

**

*

*

*

Neutrophils

**

**

*

**

*

*

*

*

*

*

ACC

BLCA

BC

CESC

CHOL

COAD

DLBC

ESCA

GBM

HNSC

KICH

KIRC

KIRP

LAML

LGG

LIHC

LUAD

LUSC

MESO

OV

PAAD

PCPG

PRAD

READ

SARC

SKCM

STAD

TGCT

THCA

THYM

UCEC

UCS

UVM

LINC00205 were negatively correlated with hsa-miR-224-5p (Fig. 10E). There were 4 target lncRNAs expression levels that are negatively correlated with hsa-miR-30a-5p, respectively EPB41L4A-AS1, PVT1, HELLPAR and DLEU2 (Fig. 10F). Based on the ceRNA hypothesis, regarding the inverse relationship between miRNA and lncRNA or mRNA (29), 14 pairs of ceRNA networks (EPB41L4A-AS1-hsa- miR-30a-5p-EFNA3, PVT1-hsa-miR-30a-5p-EFNA3, HELLPAR-hsa-miR-30a-5p-EFNA3, DLEU2-hsa- miR-30a-5p-EFNA3, OIP5-AS1-hsa-miR-30b-5p-EFNA3, SNHG16-hsa-miR-30b-5p-EFNA3, SNHG16-hsa- miR-30c-5p-EFNA3, AC239868.1-hsa-miR-30d-5p- EFNA3, EPB41L4A-AS1-hsa-miR-30d-5p-EFNA3, AL049840.4-hsa-miR-30d-5p-EFNA3, OIP5-AS1-hsa- miR-30d-5p-EFNA3, SNHG16-hsa-miR-30d-5p-EFNA3, MAGI2-AS3-hsa-miR-224-5p-EFNA3 and LINC00205-hsa- miR-224-5p-EFNA3) were constructed based on the correlation analysis results (Fig. 10G).

Analysis of genes and functions co-expressed with EFNA3 in ACC. The LinkedOmics database was used to analyze EFNA3 co-expression in ACC; under the condition of FDR<0.05, 2,000 genes were significantly positively correlated with EFNA3 expression levels (Fig. 11A), while 2,967 genes were signifi- cantly negatively correlated with EFNA3 expression levels. The genes that were positively and negatively correlated with EFNA3 expression levels in ACC are provided in Tables SXIII.

The top 50 genes most significantly positively (Fig. 11B) and negatively (Fig. 11C) correlated with EFNA3 expression levels are displayed in the heat map. Tables SXIV-XV summarizes the GO and KEGG enrichment analyses of genes positively and negatively correlated with EFNA3 expression. As shown in the functional enrichment analysis, genes positively corre- lated with EFNA3 expression were significantly enriched in pathways and biological terms including ‘Cushing syndrome’, ‘Wnt signaling pathway’, ‘C2H2 zinc finger domain binding’, ‘forebrain development’, and the ‘B-catenin-TCF complex’ (Fig. 11D). Genes negatively correlated with EFNA3 expres- sion were significantly associated with immune-related processes and molecular functions, such as ‘T-cell-mediated immunity’, ‘N-glycan processing’, ‘immunological synapse formation’ and ‘cytokine receptor activity’ (Fig. 11E).

The STRING database was used to investigate the PPI network of EFNA3; EFNA3 was associated with ephrin type-A receptor 4 (EPHA4), ephrin type-A receptor 2 (EPHA2), ephrin type-A receptor 3 (EPHA3), ephrin type-A receptor 7 (EPHA7), ephrin type-A receptor 5 (EPHA5), 1-phosphatidylinositol 4,5-bisphosphate phosphodiesterase y-1, ephrin type-A receptor, ephrin type-B receptor 1 and ephrin type-B receptor 3 (0.999, 0.948, 0.936, 0.929, 0.924, 0.914, 0.904, 0.895, 0.88 and 0.869 respectively; Fig. 11F). The confidence scores represent the calculated probability that these associated proteins have a functional interaction with EFNA3. EPHA4, EPHA2 and EPHA3 had the highest

TIL 8.

SPANDIDOS PUBLICATIONS

Figure 7. Pan-cancer analysis of drug sensitivity of EFNA3-related drugs. (A) The relationship between GDSC and CTRP drug sensitivity and EFNA3 mRNA expression. (B) FDA-approved EFNA3-related chemotherapeutic agents from CTRP drug sensitivity analysis. (C) FDA-approved EFNA3-related anticancer drugs from GDSC drug sensitivity analysis. EFNA3, ephrin-A3; GDSC, Genomics of Drug Sensitivity in Cancer; CTRP, Cancer Therapeutics Response Portal; FDA, Food and Drug Administration.

A

Correlation between drug sensitivity and mRNA expression

B

Ciclopirox

Belinostat

Valdecoxib

CTRP

GDSC

Dasatinib

Afatinib

Fluvastatin ☒

(5Z)-7-Oxozeaenol

Bosutinib

Lovastatin

A-770041

Cytarabine hydrochloride

Tivozanib

Afatinib ☒

Panobinostat

Correlation

Austocystin D

AP-24534

Tirbanibulin

AZD7762

BRD-K41597374 ☒

Paclitaxel

Alpelisib

0.25

Bleomycin (50 µM)

Erlotinib

EFNA3

Canertinib

0.00

Bortezomib

cerulenin

Neratinib

Itraconazole

-0.25

Correlation

COL-3

Bx-795

Fluorouracil

-0.3

Erlotinib

CEP701

Vincristine

0.0

Fluorouracil

CHIR-99021

Fluvastatin

Cabozantinib

Lovastatin

FQI-2

Dabrafenib

0.3

Lapatinib

Gefitinib ☒

Dasatinib

Gefitinib

Ibrutinib

Vorinostat

Ibrutinib ☒

DMOG

ISOX

Foretinib

C

Bortezomib

Selumetinib

Ko-143

HG-6-64-1

Ponatinib

Lapatinib

MG-132

Dabrafenib

Linsitinib

PFI-1

Marinopyrrole A

Cabozantinib

RDEA119

Narciclasine

Dasatinib

Selumetinib

Correlation

Neratinib

Bleomycin (50 µM)

0.2

Neuronal differentiation inducer III

Sunitinib

EFNA3

0.1

Panobinostat

Trametinib

Midostaurin

0.0

PD 153035

Vinblastine

-0.1

-0.2

Vinblastine

Pifithrin-mu

Afatinib

SB-743921

CP724714

Idelalisib

Skepinone-L

GSK690693

Valdecoxib

KIN001-102

Sunitinib

Afatinib

Vorinostat

WZ3105

Trametinib

Temsirolimus

correlation with EFNA3, suggesting that these genes may serve a promoting role in certain types of tumors. These results suggested that EFNA3 may be closely related to the occurrence and development of ACC.

Validation of ACC cell transfection efficiency. ACC cell transfection efficiency was demonstrated using RT-qPCR. In NCI-H295R and SW-13 cell lines, the mRNA expression level in EFNA3-OE group was significantly increased compared with that of the vector group, and the EFNA3 mRNA expres- sion in sh-EFNA3 group was significantly decreased compared with that of the shNC group (P<0.05; Fig. 12).

EFNA3 enhances the viability and invasiveness of ACC cells in vitro. CCK-8 assays demonstrated that EFNA3 overex- pression significantly promoted cell viability compared with that of the control group, whereas EFNA3 knockdown had the opposite effect. Flow cytometric analysis demonstrated that EFNA3 knockdown induced apoptosis and G1/S phase cell cycle arrest. Conversely, EFNA3 overexpression signifi- cantly reduced apoptosis and facilitated S-phase progression (Fig. 13A-F). In the Transwell and wound healing assays, EFNA3 overexpression significantly enhanced cell migration

capabilities, respectively. By contrast, EFNA3 knockdown significantly impaired these abilities (Fig. 14A-D).

Discussion

EFNA3, a glycolysis-associated gene, has been implicated in the progression of several malignancies, including BC, hepa- tocellular carcinoma (HCC), oral squamous cell carcinoma, pancreatic adenocarcinoma, lung adenocarcinoma (LUAD), pheochromocytoma and stomach adenocarcinoma, and has been proposed as a diagnostic and prognostic biomarker in these contexts (14,30-33). A recent multi-omics study demonstrated epigenetic regulation of EFNA3 in metastatic pheochromocytomas and paragangliomas, identifying a differentially methylated probe (cg12741345) located within the gene body of EFNA3 (34). The present study also found the cg12741345 probe among the 28 CpG sites identified in ACC, which suggested potential epigenetic dysregulation of EFNA3 in ACC pathogenesis.

To the best of our knowledge, no comprehensive pan-cancer analysis of EFNA3 incorporating multi-dimensional data has been reported. The present results demonstrated that EFNA3 is significantly upregulated in tumor tissues when compared

Table I. Correlation between EFNA3 expression levels and clinicopathological characteristics.
CharacteristicLow expression of EFNA3, n (%)High expression of EFNA3, n (%)P-value
Total patients39 (49.4)40 (50.6)
Pathological N stage0.037
037 (46.8)31 (39.2)
11 (1.3)8 (10.1)
Unknown1 (1.3)1 (1.3)
Pathological stage0.034
I6 (7.6)3 (3.8)
II23 (29.1)14 (17.7)
III5 (6.3)11 (13.9)
IV4 (5.1)11 (13.9)
Unknown1 (1.3)1 (1.3)
Tumor status<0.001
Tumor free29 (36.7)10 (12.7)
With tumor8 (10.1)30 (38.0)
Unknown2 (2.5)0 (0.0)
Primary therapy outcome0.015
Progressive disease4 (5.1)14 (17.7)
Stable disease1 (1.3)1 (1.3)
Partial response1 (1.3)0 (0.0)
Complete response30 (38)16 (20.3)
Unknown3 (3.8)9 (11.4)
Sex0.030
Female19 (24.1)29 (36.7)
Male20 (25.3)11 (13.9)
Weiss-Necrosis0.039
Absent12 (15.2)5 (6.3)
Present24 (30.4)33 (41.8)
Unknown3 (3.8)2 (2.5)
Weiss-Diffuse architecture0.026
Absent5 (6.3)14 (17.7)
Present24 (30.4)18 (22.8)
Unknown10 (12.7)8 (10.1)

The percentages presented are derived from the proportion of each variable category relative to the total sample size (n=79). Cases were categorized as unknown when source of the sample was not defined by clinical characteristics. EFNA3, ephrin-A3; N, node.

with that of adjacent normal tissues across multiple cancer types, including BLCA, CHOL and colon adenocarcinoma. However, in GBM, KICH, LAML and SKCM, EFNA3 expres- sion levels were significantly reduced. These cancer types have not been well explored regarding the biological role of EFNA3, and the clinical significance of this downregulation remains currently unclear.

EFNA3 is involved in multiple cellular functions, including tumor malignancy, angiogenesis, energy metabo- lism and intratumoral hypoxia. In HCC, EFNA3 upregulation correlates with more aggressive tumor behavior, promotion of self-renewal, proliferation, migration and tumor stemness (35). Mechanistically, under hypoxic conditions, hypoxia-inducible factor la (HIF-1a) increases EFNA3 expression in HCC by increasing copy number (12). Deng et al (14) demonstrated that

knocking down EFNA3 significantly inhibits the proliferation and glycolytic capacity of LUAD cells. Yiminniyaze et al (36) further demonstrated that EFNA3 induces epithelial-mesen- chymal transition by enhancing ERK and AKT phosphorylation levels, while upregulating MMP2 and MMP9 expression. In choroidal melanoma, EFNA3 promotes cell prolifera- tion and migration by activating the STAT3/AKT signaling pathway (37). In prostate cancer, EFNA3 knockout suppresses disease progression by reducing Ras/Braf/MEK/Erk1/2 phosphorylation levels (38). In pancreatic ductal adenocar- cinoma cells, EFNA3 enhances tumor angiogenesis and cell permeability through the Wnt/ß-catenin pathway (39). This divergent expression pattern may reflect cancer-type-specific regulatory mechanisms or TME influences. Further experi- mental studies are warranted to elucidate the role of EFNA3

SH 22

TILI ®

SPANDIDOS PUBLICATIONS

Figure 8. Association between EFNA3 expression and clinicopathological features in ACC. Association of EFNA3 expression levels with (A) Weiss-Necrosis, (B) tumor status, (C) pathological stage: I & II vs. III & IV), (D) pathological stage: I vs. II vs. III vs. IV (Kruskal-Wallis and Dunn's analysis), (E) pathological N stage and (F) pathological T stage: T1& T2 vs. T3 & T4 (Mann-Whitney U test). (G) Diagnostic value of EFNA3 in ACC. (H) Time-dependent prognostic value of EFNA3 at 1-, 3- and 5-years. (I) CI of time-dependent diagnostic value; normal group, n=128; tumor group, n=77. The error bars indicate the standard deviation. ROC analysis was performed using the pROC package; the AUC and cumulative survival rate corresponding to each time point were calculated using the time ROC package. "P<0.05, ** P<0.01 and *** P<0.001. EFNA3, ephrin-A3; ACC, adrenocortical carcinoma; AUC, area under the curve; N, node; T, tumor; TPR, true positive rate; FPR, false positive rate.

A

B

C


8

8

**

8

Expression of EFNA3 Log2 (TPM+1)

Expression of EFNA3 Log2 (TPM+1)

Expression of EFNA3 Log2 (TPM+1)

6

6

6

4

4

4

2

2

2

Absent

Present

Tumor free

With tumor

Stage I & II Pathological stage

Stage III & IV

D

Weiss-Necrosis

E

Tumor status

F

8

8

8

Expression of EFNA3 Log2 (TPM+1)

Expression of EFNA3 Log2 (TPM+1)

Expression of EFNA3 Log2 (TPM+1)

6

6

6

4

4

4

2

2

2

Stage | Stage II Stage III Stage IV Pathological stage

NO

N1

T1 & T2

T3 & T4

Pathological N stage

Pathological T stage

G

1.0

H

1.0

1.0

0.8

0.8

5.5256

0.8

Sensitivity (TPR)

Sensitivity (TPR)

0.6

0.6

AUC

0.6

0.4

0.4

0.4

0.2

EFNA3

0.2

EFNA3

AUC: 0.829

1-year (AUC = 0.764)

0.2

0.0

CI: 0.760-0.897

3-year (AUC = 0.756)

0.0

5-year (AUC = 0.812)

0.0

0.0

0.2

0.4

0.6

0.8

1.0

0.0

0.2

0.4

0.6

0.8

1.0

1

2

3

4

5

1-Specificity (FPR)

1-Specificity (FPR)

Time (years)

in these malignancies. In the future, in vivo models can be used to elucidate whether reduced EFNA3 expression confers tumor-suppressive effects or reflects compensatory biological processes, in order to expand the current understanding of EFNA3 as a context-dependent modulator in tumor biology.

Genetic alterations such as single nucleotide and CNAs are key drivers of oncogenesis and tumor progression (40). In the present pan-cancer analysis, EFNA3 exhibited a notably high mutation frequency, >40% in BC, suggesting a potential

tumor-promoting role in this context. Within the ACC cohort, the most prevalent genomic events associated with EFNA3 were elevated mRNA expression and gene amplification, both indicative of CNA-driven dysregulation. Survival analyses across pan-cancer datasets demonstrated that EFNA3 muta- tions were associated with poorer overall survival, supporting its relevance as a clinically significant genomic alteration. Specifically, patients harboring EFNA3 mutations in ACC showed significantly reduced OS and DFS compared with

A

PITA

miRanda

52

17

1

12

4

0

4

TargetScan

hsa-miR-30d-5p hsa-miR-224-5p

hsa-miR-30c-5p hsa-miR-30a-5p

hsa-miR-30b-5p hsa-miR-30e-5p

hsa-miR-330-5p hsa-miR-326

hsa-miR-145-5p hsa-miR-491-5p

hsa-miR-153-3p hsa-miR-210-3p

B

hsa-miR-145-5p vs. EFNA3, 79 samples (ACC)

hsa-miR-30b-5p vs. EFNA3, 79 samples (ACC)

hsa-miR-30a-5p vs. EFNA3, 79 samples (ACC)

Data Source: starBase v3.0 project

Data Source: starBase v3.0 project

Data Source: starBase v3.0 project

8

Regression (y = - 0.7953x + 10.3727)

8

Regression (y = - 0.8572x + 9.8073)

8

Regression (y = - 0.9537x + 15.1604)

r =- 0.365, P-value=9.26x104

r =- 0.327, P-value=3.23x10-3

r =- 0.440, P-value=5.06x10$

EFNA3, Expression level: log2[FPKM+0.01)]

6

EFNA3, Expression level: log2[FPKM+0.01)]

6

EFNA3, Expression level: log2[FPKM+0.01)]

6

4

4

4

2

2

2

0

0

0

-2

-2

-2

7

8

9

10

11

12

13

6

7

8

9

10

11

12

10

11

12

13

14

15

16

hsa-miR-145-5p, Expression level: log2(RPM+0.01)

hsa-miR-30b-5p, Expression level: log2(RPM+0.01)

hsa-miR-30a-5p, Expression level: log2(RPM+0.01)

hsa-miR-30c-5p vs. EFNA3, 79 samples (ACC)

hsa-miR-224-5p vs. EFNA3, 79 samples (ACC)

hsa-miR-30d-5p vs. EFNA3, 79 samples (ACC)

Data Source: starBase v3.0 project

Data Source: starBase v3.0 project

Data Source: starBase v3.0 project

8

Regression (y = - 1.2887x + 15.0565)

8

Regression (y = - 0.2703x + 3.5753)

8

Regression (y = - 1.2008x + 17.9154)

r =- 0.343, P-value=1.95x10-3

r =- 0.281, P-value=1.20x10-2

r =- 0.456, P-value=2.45x10-5

EFNA3, Expression level: log2[FPKM+0.01)]

6

EFNA3, Expression level: log2[FPKM+0.01)]

6

EFNA3, Expression level: log2[FPKM+0.01)]

6

4

4

4

2

2

2

0

0

0

-2

-2

-2

8.5

9

9.5

10

10.5

11

11.5

0

2.5

5

7.5

10

12.5

11

12

13

14

15

hsa-miR-30c-5p, Expression level: log2(RPM+0.01)

hsa-miR-224-5p, Expression level: log2(RPM+0.01)

hsa-miR-30d-5p, Expression level: log2(RPM+0.01)

C Target site: chr1 : 155059997-155060003Target site: chr1 : 155059556-155059562Target site: chr1 : 155059556-155059562
EFNA3-WT: 5' agucuaaaaaaaauAAACUGGAg 3'EFNA3-WT: 5' uuggauugaaaccaaGUUUACa 3'EFNA3-WT: 5' uuggauugaaaccaaGUUUACa 3'
miR-145-5P : 3' ucccuaaggacccuUUUGACCUg 5'miR-30b-5P : 3' ucgacucacauccuaCAAAUGu 5'miR-30a-5P : 3' gaaggucagcuccuaCAAAUGu 5'
Target site: chr1: 155059556-155059562Target site: chr1: 155059960-155059966Target site: chr1 : 155059556-155059562
EFNA3-WT: 5' uuuggauugaaaccaaGUUUACa 3'EFNA3-WT: 5' agugcuuugGCU-GUGACUUu 3' : | | | || | |11EFNA3-WT: 5' uuggauugaaaccaaGUUUACa 3'
miR-30c-5P : 3' cgacucucacauccuaCAAAUGu 5'miR-224-5P : 3' uugccuuggUGAUCACUGAAC 5'miR-30d-5P : 3' gaaggucagccccuaCAAAUGu 5'

Figure 9. Prediction of miRNAs targeting EFNA3 in ACC. (A) Venn diagram showing the prediction results of EFNA3 targets using the PITA, miRanda and TargetScan software. (B) Scatter plots demonstrate the miRNA-mRNA associations with significant correlation. The starBase software was used to analyze the correlation between EFNA3 and the target miRNA. (C) The TargetScan software was used to predict the potential binding site of EFNA3 to the target miRNA. EFNA3, ephrin-A3; ACC, adrenocortical carcinoma; miRNA, microRNA; WT, wild-type; chr, chromosome.

those with wild-type EFNA3, underscoring its potential role as a negative prognostic marker.

To further elucidate the genetic landscape associated with EFNA3 expression, mutation profiles between high- and low-EFNA3 expression groups were compared. CTNNB1

emerged as a differentially mutated gene, suggesting possible co-regulatory or downstream interactions. By contrast, EFNA3 expression did not significantly differ between groups stratified by TP53 or PRKAR1A mutation status, two well-established drivers in ACC, which suggested that EFNA3 regulation may

SPANDIDOS PUBLICATIONS

Figure 10. Prediction of IncRNA and ceRNA network construction in ACC. (A) Venn diagrams display the target IncRNAs of hsa-miR-145-5p, hsa-miR-30b-5p, hsa-miR-30a-5p, hsa-miR-30c-5p, hsa-miR-224-5p and hsa-miR-30d-5p respectively. The starBase software was used to analyze the correla- tions between miRNAs and the target IncRNA. Scatter plots demonstrate the miRNA-mRNA associations with significant correlation as follow, IncRNA related to (B) hsa-miR-30d-5p, (C) hsa-miR-30c-5p, (D) hsa-miR-30b-5p, (E) hsa-miR-224-5p and (F) hsa-miR-30a-5p. (G) The Sankey diagram displays the IncRNA-miRNA-mRNA EFNA3 regulatory network in line with the competitive endogenous RNA hypothesis. EFNA3, ephrin-A3; ACC, adrenocortical carcinoma; miRNA, microRNA; IncRNA, long non-coding RNA.

A

hsa-miR-145-5p

hsa-miR-30b-5p

hsa-miR-30a-5p

B

miRNet

miRNet

miRNet

asa-mik-bod-5p vs. AC239868.1. 79 samples (ACC)

hsa-mik-30d-5p vs. AL049840.4. 79 samples (ACC)

hsa-mik-30d-5p vs. EPB41444-AS1. 79 samples (ACC)

Data Source: startlane v3.@ project

Data Source: Mariase v5.0 project

Data Source: startimnie w3.@ project

Regression dy # -0.47058 + 63410

Regression fy = - 4.3867x + 8.15221

· 1-8.400, P-value=2.54=10*

Regression ly = - 0.22060 + 5.5584)

· -0.209, P-value:2.67x3b!

AL043840.A. Expression level: log.plP.M.+0.0EN

32

10

16

37

9

10

36

10

12

StarBase

StarBase

StarBase

JPX

LINC00852

1

TUGI MEG3 SNHGI MALATI

LINC01089 KCNQIOT1

PVT1 XIST

OIP5-ASI

PVTI

OIPS-ASI

DLEUZ

2

3

MUC20-OTI OTUDSB-ASI

NORAD SNHG16

HELLPAR NOP14-ASI

NEATI DLEU2

HELLPAR NOP14-ASI EPB41L4A-ASI

TBCID3PI-DHX40PI

NORAD SNHG16

TBCID3P1-DHX40P1

-3

31

1

11

14

15

.

11

12

14

11

0

u

13

N

15

ha-mail-30d-1p. Expression level: log./port/t=0.011

bsa-mit-100-5p, Expressions level: log200PM8+0.01)

hsa-miR-30c-5p

hsa-miR-224-5p

hsa-miR-30d-5p

miRNet

miRNet

hsa-miRt-30d-Sp vs. OIPS-AS1, 79 samples (ACC)

hsa-mift-30d-Sp vs. SNHG16, 79 samples (ACC)

miRNet

Data Source: starBase v3.@ project

Data Source: MarBase v3 0 projet

$

- Regression ly = - 6.3722x + 6.50711

..

SNHG36, Expression level: log2):PKOM+0.DIN

36

10

10

24

7

11

23

22

0

5

A

StarBase

StarBase

StarBase

PVT1 XIST NEATI DLEU2 NORAD

AL049840.4

SNHG16

AC008124.1

PVTI NEATI

AC239868.1

SNHG16 DLEU2

OIPS-ASI

NEATI

AC005034.3

0

HELLPAR NOP14-AS1 EPB41LAA-ASI

MALATI LINC00205

MAGI2-AS3 MCM3AP-AS1

AL137129.1

AC021078.1

MALATI

LINC00665

AL035425.3 AC012236.1 AC023632.6

AL161756.1

OIPS-ASI

STAG3L5P-PVRIG2P-PILRB

NOP14-ASI

HELLPAR

CTBPI-AS2

TBCID3PI-DHX40PI

9

11

12

13

14

15

13

12

AC018648.1

EPB41L4A-ASI

ha-mi-306-5g. Expression Irul: Ing 200PM +4.01)

C

D

E

hsa-mil-30c-5p vs. SNIG16, 79 samples (ACC)

hsa-miR-30b-5p vs. OIPS-A51, 79 samples (ACC)

hsa-miR-30b-Sp vs. SNHG 16, 79 samples (ACC)

hsa-miR-224-Sp vs. LINC00205, 79 samples (ACC)

hsa-miR-224-5p vs. MAGI2-A53, 79 samples (ACC)

Data Source: MarBase v3.0 project

Data Source: startiuse w5.@ project

Data Source: MarBase v3.0 project

Data Source: starBase v3.0 project

Data Source: starBase w5.D project

$

Regression ly - - 44648x + 6.25031

$

Regression ty = - 0.2548x + 3.42341

Regression fy . - 4.1976x + 5.1290

Regression (y = - 0.21048 + 2.74990

Regression fy = - 0.1466x + 2.03610

SNHG16. Expression level: log.29PM+: 0.0100

SNHG16, Expression Irvel: lagh://t.M.+- 0.0 2N

LINC00295, Expression level: log2;FPKUM+0.011|

MAGI2-ASK. Expression level: log.i’ll PCM +-9.0100

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.

10

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12

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.

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ha-8-300-1p. Expression level: log//go/tt-0.02)

Psa-tik-100-5p. Expression level: log/00/1+0.0.2)

Bsa-mi8-226:3p. Expression level: log//pt/t=0.021

F

hsa-miR-100-Sp vs. DLEUZ, 79 samples (ACC)

hsa-miR-30a-Sp vs. EPB4IL4A-AS1, 79 samples (ACC)

G

Data Source: tharBase v3.0 project

Data Source: vtarBase v3.0 project

AC239868.1

Regression fy = - 4.3494x 4 3.72784

Regression (y = = 6.2058% + 53382)

[PHIL4A-ASI, Expression level: log.i .P.M.+@.DEN

AL049840.4

DLEU2

hsa-miR-30d-5p

EPB41L4A-AS1

1

4

HELLPAR

4

12

14

n

0%

11

#1

16

LINC00205

hsa-md-304-1p. Expression level: log.hoursd .o.01)

hsa-ma-104-10. Expression level: loghurt+o.ot)

hsa-miR-30a-5p

EFNA3

bsa-miR-304-Sp vs. HELLPAR, 79 samples (ACC)

hsa-mik-30a-Sp vs. PVT1, 79 samples (ACC)

Data Source: startase vi o prajelt

Data Source: starBane vi.ở project

MAGI2-AS3

-Regresslan (y = - 0,6122 . 6.5562)

HELLPAR, Expression level: log29PKM+0.010

PVT L. Expression levet: log2:3pxMe+0.016

1

OIP5-AS1

5.5

PVT1

hsa-miR-224-5p

4

hsa-miR-30b-5p

41

SNHG16

10

11

12

13

1

-9

10

11

1

13

15

16

hsa-miR-30c-5p

hsa-mill-304-5g. Expression level: Ing 201840.01)

hoe-mill-10a-5p. Expression level: log 20UM+-4.01)

IncRNA

miRNA

mRNA

operate through mechanisms independent of TP53/PRKAR1A signaling.

Previous studies have shown that CTNNB1 mutations in ACC are primarily missense mutations localized to exon 3, which impair ß-catenin degradation and promote Wnt pathway activation (41,42). Future research should elucidate whether specific CTNNB1 mutation types, such as exon 3 hotspots versus null alleles, modulate EFNA3 expression or function. A mechanistic dissection of EFNA3-CTNNB1 cross-talk may yield novel insights into the oncogenic circuitry of ACC.

Unlike genomic mutations, epigenetic modifications, such as DNA methylation and RNA methylation, alter gene expres- sion without changing the DNA sequence itself (43). These modifications are increasingly recognized as pivotal regulators

of oncogenesis and tumor behavior (44). The present study identified 28 CpG methylation sites associated with EFNA3 in ACC; a CpG island methylator phenotype (CIMP) has been previously reported in ACC, with the CIMP-high subgroup associated with poorer clinical outcomes, compared with that of the CIMP-low subgroup (45,46). Aberrant DNA meth- ylation in promoter or gene body regions can silence tumor suppressor genes or activate oncogenes, thereby influencing tumor aggressiveness and therapeutic response (47). Although no methylation-targeted therapy has been clinically approved for ACC, DNA methylation inhibitors such as 5-azacytidine and decitabine have demonstrated efficacy in other types of cancer, such as BC and ACC, and are under investigation in preclinical ACC models (48-53). Decitabine demonstrates

Figure 11. Enrichment analysis of EFNA3 functional networks in ACC. (A) The Pearson test was used to identify genes highly related to EFNA3 identified in ACC. (B) The heat map shows the top 50 genes positively related to EFNA3 in the ACC cohort. (C) The heat map shows the top 50 genes negatively related to EFNA3 in the ACC cohort. (D) Enrichment of GO and KEGG terms for the top 50 genes positively related to EFNA3. (E) Enrichment of GO and KEGG terms for the top 50 genes negatively related to EFNA3. (F) Protein-protein interaction network of EFNA3. EFNA3, ephrin-A3; ACC, adrenocortical carcinoma; GO, gene ontology; KEGG, Kyoto Encyclopedia of Genes and Genomes; P.adjust, adjusted P-value.

A

EFNA3 association result

B

EFNA3

CENAA

EFNA4

6N6411

KDM4B

EMID2

W

C9orf84

KAZ

TYRO3

15

SEMA6B

SIM

RHBDL3

Q4S234E

-Log10 (pvalue)

NOV

VPREB3

EPO

10

CHRNA4

Z-Score

Group

LMX1B

RTN4R

PITX1

>3

3

C17orf96

1

2

LOC572558

NKD1

0

1

2

-1

0

ASGBI

5

TMEM120B

3

-1

2WE

-2

SYTL2

NRXN2

VGF

LEF1

MC2R

SPSB3

KCNH3

0

NLK AVD

NB4A3

CYP27B1

-1

0

1

2

PPE19

Locka LOC642852

Pearson correlation coefficient (Pearson test)

CNOT3

ATP8B3

BESK1

HSD3B2

CBX4

KIAA1644

C

MGAT4A

FMNL3

FLI1 CYSLTR1

D

Axon guidance

FILIP1L

GIMAP6

GVIN1

CSBORB

Wnt signaling pathway

FAM124B

MALL

ETS1

HLA-E

Cushing syndrome

P.adjust

PAG1

TEK

Transmembrane receptor protein

0.04

APBB2

ACSL5

RIENS

Z-Score Group

tyrosine kinase activity

0.03

VNN2

KIAA0748

>3

3

0.02

1

Transmembrane-ephrin protein receptor activity

PTPRB

2

CISH

GPRIN3

0

1

SNRK

-1

Counts

DERA

0

C2H2 zinc finger domain binding

TNFSF8

GNPTAB

3

-1

2

TLR4

-2

B-catenin-TCF complex -

4

CAPS

ARAP3

7

Sy

GIMAP8

Forebrain development

IPCEF1

SBIC

PRF1

HCG11

Androgen biosynthetic process-

ATP6V1B2

SCML4

CLIC2

DOCK2

SYNPO2

Negative regulation of hormone biosynthetic process

IL1ORA

IL2BB

5385

CO20081 CD200R1

0.05 0.10 0.15 0.20

SLC40A1

Gene Ratio

E

F

EPHB1

Amide binding

EPHA5

Peptide binding

P.adjust

Cytokine receptor activity

EPHA10

EPHB3

0.06

EPHA7

EPHA3

Rac guanyl-nucleotide exchange factor activity

0.04

Negative regulation of defense response

0.02

EFNA3

EPHA1

Counts

Positive regulation of cell killing

2

EPHA4

4

T cell mediated immunity

6

N-glycan processing -

EPHA2

PLCG1

Known interactions

Others

From curated databases

Textmining

Immunological synapse formation -

Experimentally determined

Co-expression

Predicted interactions

Protein homology

0.04 0.06 0.08 0.12 0.14 0.16

Gene neighborhood

Gene ratio

Gene fusions

Gene co-occurrence

anti-tumor effects in ACC cells at clinically relevant concen- trations by reactivating silenced genes in the 11q13 region, suggesting a role for epigenetic mechanisms in adrenocortical carcinogenesis and indicating its potential as an adjuvant treat- ment for advanced cases (49). The present data supported the

hypothesis that EFNA3 methylation patterns may contribute to ACC pathogenesis and could be leveraged as a predictive biomarker or therapeutic target.

Furthermore, significant positive correlations between EFNA3 expression and mRNA modification regulators across

SỐ TILL

SPANDIDOS PUBLICATIONS

5 3

Figure 12. Validation of EFNA3 knockdown and overexpression efficiency. Verification of EFNA3 expression efficiency after knockdown and overexpression in (A) NCI-H295R cells and (B) SW-13 cells. The error bars indicate the standard deviation. "P<0.05, ** P<0.01 and **** P<0.0001. One-way ANOVA was used for statistical analysis. Each experiment weas independently repeated three times. EFNA3, ephrin-A3; ns, not significant; OE, overexpressed; NC, negative control; sh, short hairpin.

A

NCI-H295R

B

SW-13

Relative mRNA expression

2.5

ns

**

ns

**

ns

Relative mRNA expression

1.5

2.5

1.5

Relative mRNA expression

Relative mRNA expression

ns

*

2.0

2.0

1.0

1.0

1.5

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1.0

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0.5

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0.0

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Vector

EFNA3-OE

Control

shNC

sh-EFNA3

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Vector

EFNA3-OE

Control

shNC

sh-EFNA3

Figure 13. Effects of knockdown and overexpression of EFNA3 in viability, apoptosis and cell cycle in ACC cells. Effects on (A) cell viability and (B) apoptosis in the NCI-H295R cell line. Effects on (C) cell viability and (D) apoptosis in the SW-13 cell line. Effect on cell cycle in the (E) NCI-H295R and (F) SW-13 cell lines. The error bars indicate the standard deviation. * P<0.05, ** P<0.01 and *** P<0.001. One-way ANOVA was used for statistical analysis. Each experiment weas independently repeated three times. EFNA3, ephrin-A3; ACC, adrenocortical carcinoma; OE, overexpressed; NC, negative control; sh, short hairpin.

A

B

1.4 -

NCI-H295R

0

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0

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OE-EFNA3

Q1

Q2

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Q2

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Q1

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sh-EFNA3

Apoptosis rate (%)

1.0

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Q4

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Q4

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91.8

1.85

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Annexin V-FITC

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OE-EFNA3

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OE-EFNA3

sh-NC

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Proliferation rate (%)

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Q2

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1.16

9

3.38

Q2

2.06

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Apoptosis rate (%)

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SW-13

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91.77

72.24

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91.12

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10.36

5.66

91.57

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E

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S

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60

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G2

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Vector

OE-EFNA3

F

G1

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40

100

10

ns

Percentage of cells (%)

S

Percentage of cells (%)

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80

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8

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10

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Vector

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sh-EFNA3

Vector

OE-EFNA3

pan-cancer datasets were demonstrated. In ACC specifically, several m6A modulators demonstrated expression altera- tions with prognostic implications. For instance, HNRNPC,

a known splicing regulator, was downregulated in ACC and associated with a worse prognosis (54). Conversely, ALKBH5 and YTHDF2 were upregulated and linked to

Figure 14. Effects of knockdown and overexpression of EFNA3 on the invasive and migratory capacities of ACC cells. Effects on cell migration in (A) NCI-H295R and (B) SW-13 cell lines (magnification x400; scale bar, 200 um). Effect on cell migration ability of (C) NCI-H295R and (D) SW-13 cell lines (magnification x40; scale bar, 500 um). The error bars indicate the standard deviation .*** P<0.001. One-way ANOVA was used for statistical analysis. Each experiment weas independently repeated three times. EFNA3, ephrin-A3; ACC, adrenocortical carcinoma; OE, overexpressed; NC, negative control; sh, short hairpin.

A

OE-EFNA3

sh-EFNA3

Relative cell count

2.0

Relative cell count

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0.8

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0.2

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sh-EFNA3

NCI-H295R

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sh-EFNA3

Relative cell count

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0.8

1.0

0.6

0.4

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0.2

Vector

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Vector

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sh-EFNA3

200 0m

SW13

C

D

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sh-NC

sh-EFNA3


40

0 h

Migration rate (%)

0 h

30

Migration rate (%)

30

500um

500um

20

20

48 h

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SW-13

tumor progression (54-58). METTL3, a methyltransferase, was downregulated and associated with a favorable prognosis. These findings suggested that EFNA3 may be integrated into broader epigenetic regulatory networks, including m6A RNA methylation pathways, that modulate tumor biology in ACC. Collectively, the present results suggested a complex regula- tory landscape in which EFNA3 is subject to both DNA- and RNA-level epigenetic control, offering novel insights into its diagnostic and therapeutic relevance in ACC. Future studies may explore combinations with DNA methyltrans- ferase inhibitors (such as decitabine) or m6A modulators to reverse EFNA3-driven oncogenicity, leveraging epigenetic vulnerabilities common in types of endocrine cancer.

Immunotherapy has revolutionized the treatment paradigm for various types of cancer, offering durable responses in a subset of patients, such as patients with relapsed ovarian cancer and relapsed gastric cancer (59). However, a significant proportion of individuals fail to achieve sustained benefits, which is often attributed to the complexity and heterogeneity of the TME (60,61). Immunotherapy is primarily used in patients with advanced ACC after the failure of traditional chemotherapy (62). Among these treatments, pembroli- zumab is the most studied and recommended in guidelines, although its monotherapy objective response rate remains

limited (63-65). The present study identified a significant correlation between EFNA3 expression levels and immune cell infiltration across multiple cancer types, including ACC. This suggested that EFNA3 may serve a role in modulating the immune landscape, potentially impacting tumor immune evasion and responsiveness to immunotherapeutic agents. In ACC specifically, where immune-based treatment options currently remain limited, EFNA3 may serve as a potential immunological biomarker or therapeutic target. Given its asso- ciation with immune infiltration, EFNA3 might be involved in shaping the immunosuppressive or immunoactive features of the TME. Further studies are warranted to delineate its mechanistic role in regulating immune cell recruitment, antigen presentation or checkpoint molecule expression. The correlation between EFNA3 and TME features demonstrated in the present study provide a rationale for evaluating EFNA3 not only as a diagnostic or prognostic marker but also as a modulator of tumor-immune interactions, opening avenues for combination strategies involving EFNA3-targeted agents and immune checkpoint inhibitors (such as anti-programmed cell death protein 1 and programmed cell death ligand 1) in ACC.

The ceRNA hypothesis proposes that lncRNAs can regulate gene expression by sequestering miRNAs, thereby preventing them from binding to target mRNAs (66). Increasing evidence

SPANDIDOS PUBLICATIONS

.8.

has implicated the EFNA3-centered ceRNA network in various tumor types. For example, miR-210-3p has been shown to target EFNA3, thereby modulating the PI3K/AKT pathway and influencing tumor progression in oral squamous cell carcinoma (67). Similarly, miR-210-mediated suppression of EFNA3 has been reported to affect cell proliferation and invasiveness in peripheral nerve sheath tumors (68). Under hypoxic conditions, EFNA3 can also be regulated through HIF-induced IncRNA activation, promoting metastatic spread in BC (69).

The present study constructed a IncRNA-miRNA-EFNA3 regulatory axis in ACC, highlighting novel non-coding RNA molecules such as OIP5-AS1 and hsa-miR-30d-5p. Previous studies have shown that OIP5-AS1 can act as a ceRNA to modulate oncogenic signaling in endocrine tumors, while miR-486-3p is downregulated in adrenocortical neoplasms and may serve as a tumor suppressor (70,71). The ceRNA network involving EFNA3 identified in the present analysis demonstrated a potential mechanism of post-transcriptional regulation that could contribute to tumor progression, immune modulation and drug resistance in ACC. Furthermore, targeting the IncRNA-miRNA-EFNA3 regulatory axis may have thera- peutic potential. For example, salazosulfapyridine has been proposed to exert anticancer effects in ACC by interacting with the OIP5-AS1-miR-92a-3p-SLC7A11 pathway (72). The present findings underscored the potential of EFNA3-centered ceRNA regulatory networks as diagnostic tools and therapeutic targets in ACC, warranting further functional validation.

Drug repurposing offers a cost-effective and time-efficient strategy to identify new therapeutic options for rare and refrac- tory malignancies such as ACC. In the present study, drug sensitivity correlation analysis was performed based on EFNA3 expression was performed, identifying 24 EFNA3-associated compounds in the CTRP database and 14 in the GDSC data- base. Notably, EFNA3 expression was significantly correlated with sensitivity to HMG-COA reductase inhibitors (statins), which have gained interest for their potential antitumor effects (73,74). Statins, primarily used to treat hypercho- lesterolemia, have demonstrated tumor-suppressive effects in multiple cancer types, including HCC, breast, lung and colorectal cancer (75-80). Mechanistically, statins exert anti- tumor effects through inhibition of the mevalonate pathway, leading to suppression of AKT/NF-KB signaling, induction of apoptosis via caspase cascade activation and impairment of metastatic potential through modulation of MAPK and mTOR pathways (81-88). Simvastatin, for example, has been shown to activate AMPK, upregulate p21 and induce apoptosis in HCC cells (86). HMG-COA reductase inhibitors reduce isoprenoid synthesis by inhibiting the mevalonate pathway, thereby affecting the tumor procession (89).

Despite this promising pharmacological profile, limited studies have examined the application of statins in endocrine malignancies, particularly in ACC. Given the dependence of ACC cells on cholesterol biosynthesis and isoprenoid metabo- lism (90), the mevalonate pathway represents a potential target. Furthermore, given the key role of EFNA3 in glycolysis, combining EFNA3 inhibition with glycolytic inhibitors or statins represents a metabolic ‘double-hit’ strategy against the Warburg-dependency of ACC. The present results highlight EFNA3 as a potential biomarker for predicting statin sensitivity

in ACC. The therapeutic implications of this finding warrant further validation through in vitro mechanistic assays and in vivo efficacy studies. Furthermore, integrating statins with EFNA3-targeted strategies may provide a synergistic approach to disrupt tumor metabolism and reduce ACC aggressiveness.

The Wnt/B-catenin signaling cascade serves a pivotal role in ACC by regulating tumor cell proliferation, migration and metabolic reprogramming. Dysregulation of Wnt/ß-catenin pathway, commonly through activating mutations in the CTNNB1 gene, is a hallmark of ACC pathogenesis (91,92). In the present transcriptome-based co-expression analysis, EFNA3 was closely associated with genes involved in Wnt signaling, suggesting a potential regulatory interaction. Specifically, EFNA3 expression was significantly increased in CTNNB1-mutated samples, demonstrating an association between EFNA3 activity and Wnt/ß-catenin pathway dysregu- lation. Previous research has demonstrated that ß-catenin and Transcription Factor 4 modulate the expression of EphB receptors and their ligands, including ephrin-B1, thereby orchestrating spatial organization along epithelial axes such as the crypt-villus axis in colorectal cancer (93). The present findings suggested a similar interaction may exist between EFNA3 and ß-catenin in ACC, which potentially contributes to malignant transformation. Furthermore, EFNA3 is a glycol- ysis-related gene, and the Wnt/ß-catenin pathway is a known driver of metabolic reprogramming in cancer cells (94). This pathway enhances aerobic glycolysis by upregulating glyco- lytic enzymes, promoting a tumor-favorable microenvironment characterized by increased lactate production and glucose uptake (95-101). In colon and breast cancer, activation of Wnt signaling induces pyruvate dehydrogenase kinase 1 expression and modulates adipogenic enzymes, respectively, reinforcing glycolytic flux and tumor proliferation (96-98).

The present in vitro experiments demonstrated that EFNA3 promotes invasive behavior in ACC cells. These data suggested that EFNA3 may act as a downstream effector or modulator of Wnt/ß-catenin signaling to coordinate both metabolic and invasive phenotypes in ACC. Future mechanistic studies are warranted to dissect the precise molecular interactions between EFNA3, ß-catenin and glycolysis-related signaling pathways in ACC progression. These findings present EFNA3 not only as a key mediator of Wnt-driven ACC pathogenesis but also as a potential node for combinatorial therapeutic intervention. Given the established challenges in targeting Wnt/B-catenin signaling directly in endocrine tumors, primarily the disrup- tion of normal somatic stem cell function critical for cellular repair and tissue homeostasis (102), EFNA3 inhibition offers a tractable approach to disrupt downstream oncogenic outputs (such as metabolic reprogramming and invasion) while potentially synergizing with Wnt pathway modulators or endocrine-disrupting agents.

Despite the comprehensive nature of the present study, several limitations should be acknowledged. First, the bioin- formatics analyses were primarily based on the relatively small TCGA-ACC cohort. Future studies incorporating larger, multi-center datasets are needed to strengthen the robustness and generalizability of these findings. Although the integrative bioinformatics and in vitro findings suggested that EFNA3 is associated with enhanced sensitivity to HMG-COA reductase inhibitors, clinical evidence remains lacking. Large-scale,

randomized controlled trials are needed to validate the thera- peutic efficacy of these agents and safety in patients with ACC. Second, the ceRNA regulatory network involving EFNA3 was constructed through computational predictions and partially supported by molecular data. however, extensive experimental validation, particularly through gain and loss-of-function; assays in vivo, is required to confirm biological relevance and establish causal relationships between EFNA3 and these pathways. Third, although significant epigenetic alterations associated with EFNA3 expression in ACC were observed, the potential of DNA methylation inhibitors as a therapeutic strategy remains unexplored in clinical settings. Additional preclinical studies are necessary to determine whether demethylating agents can reverse EFNA3-mediated oncogenic effects. While the present in vitro experiments demonstrated EFNA3 enhances ACC cell invasiveness, the absence of in vivo validation remains a key constraint. The precise molecular mechanism governing the interplay between EFNA3, Wnt/ß-catenin signaling and metabolic reprogram- ming requires further elucidation through mechanistic studies in animal models complemented by patient-derived organoids.

Future research should also explore the feasibility of targeting EFNA3 as a multi-modal biomarker for ACC prognosis, immu- nomodulation and drug responsiveness. Future research should focus on verifying the synergistic potential of EFNA3-targeted therapy with four major categories of drugs: Immune checkpoint inhibitors (to reverse immunosuppression), epigenetic modula- tors (to regulate the methylation/m6A network), metabolic disruptors (to block glycolysis and mevalonate pathways) and endocrine-specific drugs (adrenal diuretics and steroid synthesis inhibitors). This is essential to overcome ACC drug resistance, achieve synergistic effects, and are key to translating the present findings into clinically actionable strategies.

The present study identified EFNA3 as a potential onco- genic driver and prognostic biomarker in adrenocortical carcinoma. Through integrative bioinformatics analyses and in vitro validation, it was demonstrated that EFNA3 may modulate tumor invasiveness, potentially through its interac- tion with the Wnt/B-catenin signaling pathway and glycolytic reprogramming. EFNA3 expression was also associated with immune cell infiltration, epigenetic alterations and drug sensitivity, particularly to HMG-COA reductase inhibitors, highlighting its potential as a multifaceted therapeutic target. Furthermore, construction of a ceRNA regulatory network provided novel insights into the post-transcriptional control of EFNA3 in ACC. These findings collectively support the trans- lational relevance of EFNA3 and warrant further mechanistic and clinical investigation.

Acknowledgements

Not applicable.

Funding

The present study was supported by the Natural Science Research in Shanxi Province (grant no. 202203021211072), Postgraduate Practice and Innovation Project (grant no. 2024SJ173) and the Task Book of High-Level Research Results Continuation Funding Project from Shanxi

Bethune Hospital (Shanxi Medical Science Academy; grant no. 2024GSPYJ04).

Availability of data and materials

The data generated in the present study may be requested from the corresponding author.

Authors’ contributions

YT, XL and JS designed and implemented the study. YT and YZ performed acquisition, analysis or interpretation of data for the work. YT, XL, YZ and JS contributed to drafting the work or revising it critically for important intellectual content. JS supervised the project, acquired funding and provided final approval of the published version. YT and XL confirm the authenticity of all the raw data. All authors agreed to be accountable for all aspects of the work in ensuring that ques- tions related to the accuracy or integrity of any part of the work are appropriately investigated and resolved All authors have read and approved the final manuscript.

Not applicable

Not applicable

Competing interests

The authors declare that they have no competing interests.

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